| Gastric variceal bleeding uncovering a rare association of CREST syndrome, primary biliary cirrhosis, nodular regenerative hyperplasia and pulmonary hypertension. | |
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MedLine Citation:
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PMID: 20485183 Owner: NLM Status: In-Process |
Abstract/OtherAbstract:
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A 73-year-old woman was admitted after the first upper gastric tract haemorrhage due to gastric variceal bleeding. A CREST syndrome associated with Hashimoto's thyroiditis, Gougerot-Sjögren syndrome, cryoglobulinaemia and complicated with severe pulmonary hypertension was diagnosed. Liver histology found precirrhotic lesions of primary biliary cirrhosis (PBC) and nodular regenerative hyperplasia (NRH). Collagen diseases are often associated with liver test abnormalities and liver disease usually associated with CREST syndrome is PBC. NRH has been found in association with collagen diseases but also with haematological diseases or drugs or with autoimmune diseases, such as PBC. This case shows the association of PBC and NRH with porto pulmonary hypertension in CREST syndrome. |
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Authors:
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Etienne Riviere; Julien Vergniol; Armel Reffet; Nicolas Lippa; Brigitte Le Bail; Victor de Ledinghen |
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Publication Detail:
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Type: Journal Article |
Journal Detail:
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Title: European journal of gastroenterology & hepatology Volume: 22 ISSN: 1473-5687 ISO Abbreviation: Eur J Gastroenterol Hepatol Publication Date: 2010 Sep |
Date Detail:
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Created Date: 2010-08-05 Completed Date: - Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 9000874 Medline TA: Eur J Gastroenterol Hepatol Country: England |
Other Details:
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Languages: eng Pagination: 1145-8 Citation Subset: IM |
Affiliation:
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Service d'Hépato-Gastroentérologie, Hôpital du Haut-Lévêque, 33604 Pessac cedex, France. |
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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