| Functional 'composite' pheochromocytoma-ganglioneuroma presenting as a pancreatic mass. | |
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MedLine Citation:
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PMID: 22687375 Owner: NLM Status: In-Data-Review |
Abstract/OtherAbstract:
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Pheochromocytomas rarely have 'composite' forms in which they demonstrate histologic features of a typical paraganglioma in combination with those of a neural component. Extra-adrenal 'composite' pheochromocytomas are distinctly uncommon. We describe herein a unique case of a 34-year-old female patient with type 1 neurofibromatosis who presented with abdominal pain and paroxysmal hypertension. Imaging revealed a pancreatic mass with biliary and pancreatic ductal dilatation and a hormonal assay led to the diagnosis of functional pheochromocytoma. She underwent surgical resection and histopathology revealed a composite paraganglioma-ganglioneuroma. Clinical, biochemical and radiological aspects of this rare tumor and its association with neurofibromatosis and other hereditary cancer syndromes are discussed. |
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Authors:
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Shounak Majumder; Joanna Grabska; Guru Trikudanathan; Pamela Kowalczyk; Elena Stoica-Mustafa; Constantin A Dasanu |
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Publication Detail:
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Type: Journal Article Date: 2012-02-08 |
Journal Detail:
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Title: Pancreatology : official journal of the International Association of Pancreatology (IAP) ... [et al.] Volume: 12 ISSN: 1424-3911 ISO Abbreviation: Pancreatology Publication Date: 2012 May |
Date Detail:
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Created Date: 2012-06-12 Completed Date: - Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 100966936 Medline TA: Pancreatology Country: Switzerland |
Other Details:
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Languages: eng Pagination: 211-4 Citation Subset: IM |
Copyright Information:
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Copyright © 2012 IAP and EPC. Published by Elsevier B.V. All rights reserved. |
Affiliation:
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Department of Internal Medicine, University of Connecticut, 263 Farmington Avenue, Farmington, CT 06030, United States. |
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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