| Fragile lung in the Marfan syndrome. | |
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MedLine Citation:
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PMID: 1013948 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Two cases of the Marfan syndrome presented with spontaneous pneumothorax. Both had chest radiographs showing bilateral bullae in the upper lung zones and pulmonary function tests consistent with mild emphysema. There were dereases in forced expiratory flow rates at low lung volumes, carbon monoxide transfer factor, and lung elastic recoil. It is suggested that pneumothorax and bullous emphysema in this syndrome are caused by a weakness in the pulmonary connective tissue framework. |
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Authors:
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J A Turner; N N Stanley |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Thorax Volume: 31 ISSN: 0040-6376 ISO Abbreviation: Thorax Publication Date: 1976 Dec |
Date Detail:
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Created Date: 1977-03-21 Completed Date: 1977-03-21 Revised Date: 2009-11-18 |
Medline Journal Info:
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Nlm Unique ID: 0417353 Medline TA: Thorax Country: ENGLAND |
Other Details:
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Languages: eng Pagination: 771-5 Citation Subset: IM |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adult Humans Male Marfan Syndrome / complications* Pneumothorax / etiology* Pulmonary Emphysema / etiology Respiratory Function Tests |
| Comments/Corrections | |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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