Document Detail


Fragile X syndrome and 22q11.2 microdeletion in the same sibship.
MedLine Citation:
PMID:  11186890     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We present a family with an unusual association of two frequent genetic disorders, 22q11.2 microdeletion and fragile X syndrome, originating from the same parent. Our observation confirms the wide intrafamilial clinical variability of the 22q11.2 microdeletion and illustrates the difficulty of the clinical diagnosis for the fragile X syndrome in affected females.
Authors:
C Missirian; A Moncla; M A Voelckel; V Ravix; N Philip
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  American journal of medical genetics     Volume:  95     ISSN:  0148-7299     ISO Abbreviation:  Am. J. Med. Genet.     Publication Date:  2000 Dec 
Date Detail:
Created Date:  2001-01-12     Completed Date:  2001-02-22     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  7708900     Medline TA:  Am J Med Genet     Country:  United States    
Other Details:
Languages:  eng     Pagination:  358-60     Citation Subset:  IM    
Affiliation:
Département de Génétique Médicale, H pital de la Timone-Enfants, Marseille, France. cmissirian@ap-hm.fr
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MeSH Terms
Descriptor/Qualifier:
Child, Preschool
Chromosome Deletion*
Chromosomes, Human, Pair 22 / genetics*
DiGeorge Syndrome / genetics
Female
Fragile X Syndrome / genetics*
Humans
Infant
Infant, Newborn
Male
Mental Retardation / genetics
Mutation / genetics
Nuclear Family*
Pedigree
Pregnancy
Tetralogy of Fallot / genetics

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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