Document Detail


First reported cases of intravascular large cell lymphoma of the NK cell type: clinical, histologic, immunophenotypic, and molecular features.
MedLine Citation:
PMID:  15743739     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Most cases of intravascular large cell lymphoma are of B-cell phenotype, with a few cases of T-cell lineage and rare cases with histiocytic features described. A definitive natural killer (NK) cell variant has not been recognized. This report is the first to describe the clinical, histologic, immunophenotypic, and molecular features of 2 cases of intravascular lymphoma with an NK cell phenotype (CD3epsilon+, CD2+, CD7+, CD56+, T-cell intracytoplasmic antigen-1+, perforin+, granzyme B+, CD20-, CD4-, CD5-, CD8-, T-cell receptor [TCR]betaF1-). Molecular studies for TCR gene rearrangements revealed a germline configuration. A 41-year-old man had erythematous plaque-like subcutaneous lesions of the lower extremities in which biopsy revealed Epstein-Barr virus-positive intravascular lymphoma. Following chemotherapy and stem cell transplantation, he was alive with no evidence of disease at 1 year. A 47-year-old woman had myalgias, arthralgias, weakness, fever, altered mental status, and pancytopenia. Bone marrow biopsy demonstrated intravascular lymphoma. Therapy was initiated; however, her condition deteriorated rapidly, and she died. Autopsy revealed involvement of multiple organs, including brain, kidneys, ovaries, and bone marrow. These cases represent the first documented examples of an NK cell variant of intravascular lymphoma.
Authors:
Huiqing Wu; Jonathan W Said; Elizabeth D Ames; Chen Chen; Valerie McWhorter; Peter Chen; Violette Ghali; Geraldine S Pinkus
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  American journal of clinical pathology     Volume:  123     ISSN:  0002-9173     ISO Abbreviation:  Am. J. Clin. Pathol.     Publication Date:  2005 Apr 
Date Detail:
Created Date:  2005-03-03     Completed Date:  2005-05-12     Revised Date:  2007-11-15    
Medline Journal Info:
Nlm Unique ID:  0370470     Medline TA:  Am J Clin Pathol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  603-11     Citation Subset:  AIM; IM    
Affiliation:
Department of Pathology, Brigham and Women's, Hospital and Harvard Medical School, Boston, MA 02115, USA.
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MeSH Terms
Descriptor/Qualifier:
Adult
Antigens, CD / analysis
Brain / blood supply,  pathology
Female
Gene Rearrangement
Genes, T-Cell Receptor
Humans
Immunohistochemistry
Immunophenotyping
Killer Cells, Natural / metabolism*,  pathology*
Lymphoma, Large B-Cell, Diffuse / genetics,  metabolism*,  pathology*
Male
Middle Aged
Polymerase Chain Reaction
Skin / blood supply,  pathology
Chemical
Reg. No./Substance:
0/Antigens, CD

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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