Document Detail


Fatty acid desaturase 2 promoter mutation is not responsible for Δ6-desaturase deficiency.
MedLine Citation:
PMID:  21629299     Owner:  NLM     Status:  Publisher    
Abstract/OtherAbstract:
Dietary essential polyunsaturated fatty acids (PUFAs) require fatty acid desaturases (FADS) for conversion to long-chain PUFAs (LCPUFAs), which are critical for many aspects of human health. A Δ6-desaturase deficiency in a single patient was attributed to an insertion mutation in the FADS2 promoter. Later population studies have shown this thymidine nucleotide (T) insertion to be a common polymorphism (rs3834458). We examined correlations between rs3834458 variants and fatty acid evidence of FADS2 activity in a cohort of rheumatoid arthritis patients selected for low or nil consumption of n-3 LCPUFA as fish or fish oil. The presence of the T allele was associated with higher FADS2 activity, as indicated by higher conversion of plasma n-3 PUFA to LCPUFA. However, the T-insertion/deletion polymorphism did not affect FADS2 promoter activity in luciferase reporter assays in HepG2 or NIH/3T3 cells. Our results indicate that the polymorphism rs3834458 does not appear to directly affect FADS2 promoter activity and is not responsible for a previously reported Δ6-desaturase deficiency.European Journal of Human Genetics advance online publication, 1 June 2011; doi:10.1038/ejhg.2011.104.
Authors:
Melissa K Gregory; Susan E Lester; Rebecca J Cook-Johnson; Robert A Gibson; Susanna M Proudman; Leslie G Cleland; Michael J James
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Publication Detail:
Type:  JOURNAL ARTICLE     Date:  2011-6-01
Journal Detail:
Title:  European journal of human genetics : EJHG     Volume:  -     ISSN:  1476-5438     ISO Abbreviation:  -     Publication Date:  2011 Jun 
Date Detail:
Created Date:  2011-6-1     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9302235     Medline TA:  Eur J Hum Genet     Country:  -    
Other Details:
Languages:  ENG     Pagination:  -     Citation Subset:  -    
Affiliation:
Rheumatology Unit, Royal Adelaide Hospital, Adelaide, South Australia, Australia.
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