Document Detail


Fatty acid composition of hepatic triglycerides in Reye's syndrome: implications for hepatic desaturase abnormalities.
MedLine Citation:
PMID:  1819459     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Serum NEFA profiles in Reye's syndrome are reportedly unique with a disproportionate percent made up of polyunsaturated fatty acids some of which are not ordinarily found in the serum. This pattern is also reflected in the serum triglyceride composition as well. As the liver is probably the sole source of the serum triglyceride in Rye's syndrome because patients are vomiting or in coma, the fatty acid acid composition of the liver triglyceride was examined for insight regarding the lipid abnormalities in this disease. Palmitic acid (16:0) and the sum of all the saturated fatty acids in the liver triglycerides were significantly decreased whereas the sum of the monoenoic fatty acids and the products of delta 9 desaturase activity were increased in Reye's samples. When these data were compared to the fatty acid composition of the serum triglyceride from a separate cohort of Reye's and control subjects, certain inferences regarding hepatic delta 9, delta 6, delta 5, and delta 4 desaturase activities and the elongases can be drawn from the liver and serum triglyceride fatty acid profiles which are unique. Collectively, these data reflect considerable intrahepatic fatty acid desaturation and elongation activity and/or acyl transfer from lipid to lipid of various polyunsaturated fatty acids in Reye's syndrome.
Authors:
E S Kang; S B Johnson; R T Holman
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Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.    
Journal Detail:
Title:  Clinica chimica acta; international journal of clinical chemistry     Volume:  204     ISSN:  0009-8981     ISO Abbreviation:  Clin. Chim. Acta     Publication Date:  1991 Dec 
Date Detail:
Created Date:  1992-07-30     Completed Date:  1992-07-30     Revised Date:  2009-11-19    
Medline Journal Info:
Nlm Unique ID:  1302422     Medline TA:  Clin Chim Acta     Country:  NETHERLANDS    
Other Details:
Languages:  eng     Pagination:  167-77     Citation Subset:  IM    
Affiliation:
Department of Pediatrics, University of Tennessee-Memphis 38163.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Child
Child, Preschool
Fatty Acid Desaturases / metabolism*
Fatty Acids / analysis,  blood,  metabolism*
Fatty Acids, Nonesterified / blood
Humans
Infant
Liver / metabolism*
Reference Values
Reye Syndrome / blood,  enzymology,  metabolism*
Triglycerides / analysis,  blood,  metabolism*
Grant Support
ID/Acronym/Agency:
DK-38321/DK/NIDDK NIH HHS; NS-14304/NS/NINDS NIH HHS; P30 AM34931/AM/NIADDK NIH HHS
Chemical
Reg. No./Substance:
0/Fatty Acids; 0/Fatty Acids, Nonesterified; 0/Triglycerides; EC 1.14.19.-/Fatty Acid Desaturases

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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