Document Detail

Fatal mesenteric fibromuscular dysplasia: a case report and review of the literature.
MedLine Citation:
PMID:  15159274     Owner:  NLM     Status:  MEDLINE    
Fibromuscular dysplasia is a rare nonatherosclerotic, noninflammatory angiopathy of uncertain etiology and high morbidity. Because of its propensity to affect medium-sized vessels in a variety of locations, presenting symptoms may vary substantially, resulting in a delayed or missed diagnosis. We describe a 57-year-old woman who, on multiple occasions, presented with progressive gastrointestinal symptoms and eventually underwent surgical revascularization for celiac and superior mesenteric artery stenosis of uncertain etiology. Her postoperative course was complicated by bowel ischemia, multiple organ failure, and death. Autopsy findings proved useful in determining the underlying disease process and cause of death. This case report and a review of the literature illustrate the high morbidity and mortality that are caused by mesenteric fibromuscular dysplasia, the challenge in establishing a correct diagnosis, and the importance of early detection and treatment.
Carrie K Guill; Diana C Benavides; Chet Rees; Andrew Z Fenves; Elizabeth C Burton
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Archives of internal medicine     Volume:  164     ISSN:  0003-9926     ISO Abbreviation:  Arch. Intern. Med.     Publication Date:  2004 May 
Date Detail:
Created Date:  2004-05-25     Completed Date:  2004-06-15     Revised Date:  2005-11-16    
Medline Journal Info:
Nlm Unique ID:  0372440     Medline TA:  Arch Intern Med     Country:  United States    
Other Details:
Languages:  eng     Pagination:  1148-53     Citation Subset:  AIM; IM    
Department of Dermatology, University of Texas Southwestern Medical Center, Dallas, TX, USA.
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MeSH Terms
Abdominal Pain / diagnosis,  etiology
Biopsy, Needle
Celiac Artery / pathology*
Disease Progression
Fatal Outcome
Fibromuscular Dysplasia / complications,  pathology*,  therapy
Laparotomy / methods
Mesenteric Vascular Occlusion / complications,  pathology*,  radiography*,  surgery
Middle Aged
Risk Assessment
Severity of Illness Index
Vascular Surgical Procedures / methods

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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