Document Detail


Familial occurrence of ptosis, nasal speech, prominent ears, hand anomalies and learning problems.
MedLine Citation:
PMID:  20362700     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We describe a four-generation family in whom 5 members show the combination of a large head, ptosis, nasal speech that sometimes goes along with a cleft palate, full cheeks, small mouth, and prominent ears, and who also have learning problems. We evaluated three affected members in detail and found them to have in addition a partial cutaneous syndactyly between the third and fourth fingers, an increased distance between second and third finger, and a decreased smell. We have not been unable to find other patients described in literature with the same combination of features, and suggest this to represent a hitherto unrecognizable entity. Pattern of inheritance is likely to be autosomal dominant.
Authors:
Elga F Belligni; Raoul C M Hennekam
Publication Detail:
Type:  Case Reports; Journal Article     Date:  2010-04-01
Journal Detail:
Title:  European journal of medical genetics     Volume:  53     ISSN:  1878-0849     ISO Abbreviation:  Eur J Med Genet     Publication Date:    2010 Jul-Aug
Date Detail:
Created Date:  2010-07-12     Completed Date:  2010-10-25     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101247089     Medline TA:  Eur J Med Genet     Country:  Netherlands    
Other Details:
Languages:  eng     Pagination:  192-6     Citation Subset:  IM    
Copyright Information:
Copyright 2010 Elsevier Masson SAS. All rights reserved.
Affiliation:
Department of Pediatrics, University of Torino, Torino, Italy.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adult
Blepharoptosis / genetics*,  pathology
Child
Child, Preschool
Ear / abnormalities*,  pathology
Family
Female
Genetic Predisposition to Disease*
Hand Deformities / genetics*,  pathology
Humans
Infant, Newborn
Learning Disorders / genetics*,  pathology
Male
Middle Aged
Pedigree
Prognosis
Speech Disorders / genetics*,  pathology

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Effect of different glucose concentrations on proteome of Saccharomyces cerevisiae.
Next Document:  Effect of HIP/ribosomal protein L29 deficiency on mineral properties of murine bones and teeth.