| Extracardiac medical and neuromuscular implications in restrictive cardiomyopathy. | |
| | |
MedLine Citation:
|
PMID: 17680617 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
|
Restrictive cardiomyopathy (RCMP) is characterized by restrictive filling and reduced diastolic volume of either or both ventricles with normal or near-normal systolic function and wall thickness. It may occur idiopathically or as a cardiac manifestation of systemic diseases such as scleroderma, amyloidosis, Churg-Strauss syndrome, cystinosis, sarcoidosis, lymphoma, Gaucher's disease, hemochromatosis, Fabry's disease, pseudoxanthoma elasticum, hypereosinophilic syndrome, carcinoid, Noonan's syndrome, reactive arthritis, or Werner's syndrome and various neuromuscular disorders. Whereas in idiopathic RCMP the therapeutic options are only treatment of cardiac congestion, in cases with an underlying disorder, a causal therapy may be available. Patients with RCMP should be investigated as soon as the cardiac diagnosis is established for extracardiac diseases to detect a possibly treatable cause of RCMP before the disease becomes intractable. These investigations include a diligent clinical history and examination, blood tests, and ophthalmologic, otologic, dermatologic, gastroenterologic, nephrologic, hematologic, and neurologic examinations. If extracardiac examinations do not reveal a plausible cause for RCMP, endomyocardial biopsy is indicated. |
| | |
Authors:
|
Claudia Stöllberger; Josef Finsterer |
Related Documents
:
|
9090407 - Large vestibular aqueduct syndrome with high ct density and high mr signal intensity. 21409937 - Kartagener's syndrome and acute appendicitis. 21495177 - Observations on intelligence and behavior in 15 patients with legius syndrome. 8874917 - The anaesthetic management of a patient with emery-dreifuss muscular dystrophy. 8418667 - Phenotype of cranioectodermal dysplasia with different hair and bone abnormalities. 17852457 - Pearson syndrome in an infant heterozygous for c282y allele of hfe gene. |
Publication Detail:
|
Type: Journal Article; Review |
Journal Detail:
|
Title: Clinical cardiology Volume: 30 ISSN: 0160-9289 ISO Abbreviation: Clin Cardiol Publication Date: 2007 Aug |
Date Detail:
|
Created Date: 2007-08-13 Completed Date: 2008-03-21 Revised Date: - |
Medline Journal Info:
|
Nlm Unique ID: 7903272 Medline TA: Clin Cardiol Country: United States |
Other Details:
|
Languages: eng Pagination: 375-80 Citation Subset: IM |
Copyright Information:
|
(c) 2007 Wiley Periodicals, Inc. |
Affiliation:
|
Medizinische Abteilung, Krankenanstalt Rudolfstiftung, Vienna, Austria. claudia.stoellberger@chello.at |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
Biological Markers
/
blood Biopsy Cardiomyopathy, Restrictive / complications*, diagnosis, genetics, physiopathology*, therapy Echocardiography Electrocardiography Endocardium / pathology Genetic Predisposition to Disease Heart Catheterization Humans Myocardium / pathology Neuromuscular Diseases / etiology* Stroke Volume Ventricular Pressure |
| Chemical | |
Reg. No./Substance:
|
0/Biological Markers |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: Personnel exposure to violence in hospital emergency wards: a routine activity approach.
Next Document: Thoughts about the abnormalities in the electrocardiogram of patients with acute myocardial infarcti...