Document Detail


Extra-acral cutaneous/soft tissue sclerosing perineurioma: an under-recognized entity in the differential of CD34-positive cutaneous neoplasms.
MedLine Citation:
PMID:  20412342     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
BACKGROUND: Perineuriomas are an uncommon group of tumors composed of perineurial cells of peripheral nerve sheath lineage. Variants include soft tissue (extraneural), intraneural, sclerosing, reticular and plexiform forms. Sclerosing perineuriomas have been reported to occur almost exclusively on the hands of young men. Herein, we report three extra-acral cutaneous/soft tissue perineuriomas that show significant associated sclerosis.
METHODS: Skin biopsy specimens from three patients were evaluated for cytomorphology and degree of associated sclerosis, which was classified as either focal or diffuse. Immunohistochemical expression of epithelial membrane antigen (EMA), CD34 and S-100 was also assessed to facilitate further classification.
RESULTS: Histopathologically, the tumors showed both focal and diffuse sclerosis, and lesional cells were generally spindled in shape. Immunohistochemical staining showed diffuse positivity for CD34 and focal or diffuse positivity for EMA. The cells uniformly lacked expression of S-100 protein.
CONCLUSIONS: Sclerosing perineuriomas can occur in extra-acral locations and should be considered in the differential of EMA-positive cutaneous spindle-cell proliferations. It is also important to recognize that perineuriomas can express CD34 and should be considered in the differential diagnosis of CD34-positive cutaneous neoplasms.
Authors:
Melanie D Fox; Briana C Gleason; Antoinette B Thomas; Thomas A Victor; Thomas L Cibull
Publication Detail:
Type:  Journal Article     Date:  2010-04-12
Journal Detail:
Title:  Journal of cutaneous pathology     Volume:  37     ISSN:  1600-0560     ISO Abbreviation:  J. Cutan. Pathol.     Publication Date:  2010 Oct 
Date Detail:
Created Date:  2010-08-19     Completed Date:  2010-12-02     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0425124     Medline TA:  J Cutan Pathol     Country:  Denmark    
Other Details:
Languages:  eng     Pagination:  1053-6     Citation Subset:  IM    
Affiliation:
Department of Pathology, Northshore University HealthSystem, Evanston, IL, USA.
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MeSH Terms
Descriptor/Qualifier:
Aged, 80 and over
Antigens, CD34 / metabolism
Diagnosis, Differential
Female
Humans
Immunohistochemistry
Middle Aged
Mucin-1 / metabolism
Nerve Sheath Neoplasms / metabolism,  pathology*
Skin Neoplasms / metabolism,  pathology*
Soft Tissue Neoplasms / metabolism,  pathology*
Tumor Markers, Biological / analysis
Chemical
Reg. No./Substance:
0/Antigens, CD34; 0/Mucin-1; 0/Tumor Markers, Biological

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