| Evaluation of findings in Crouzon's syndrome. | |
| | |
MedLine Citation:
|
PMID: 12045969 Owner: NLM Status: Publisher |
Abstract/OtherAbstract:
|
PURPOSE. The purpose of this study was to investigate the ocular, facial and radiological signs of Crouzon's syndrome in a group of older patients who had not undergone previous craniofacial surgery. METHODS. Six cases of Crouzon's syndrome, four of whom belonged to a three-generation family, were examined systemically, ophthalmologically and roentgenographically; five of these cases were additionally evaluated with computed tomography and compared with Apert syndrome. RESULTS. On radiologic evaluation, all cases had synostosis of all cranial sutures and fontanelles and brachycephalic skulls, crowding of the upper teeth due to maxillary hypoplasia, and serious nasal septum deviation. Bilateral ethmoidal, maxillary and sphenoidal chronic sinusitis was found in 50% of cases. Three patients had hypertelorism and two others had a tendency toward hypertelorism. The typical facial appearance with shallow orbits, globe protrusion and exorbitism was present in all cases. Two of them had V-pattern exotropia while the other four were orthophoric. The single case with mental retardation had bilateral cataract. CONCLUSION. Crouzon's syndrome can present with different findings and must be evaluated multidisciplinarly. |
| | |
Authors:
|
Ayse Gül Koçak Altintas; Fatma Gül Gül Aksoy; Cumhur S. Altintas; Inci Koçak Midillioglu; Sunay Duman |
Related Documents
:
|
21647039 - Acute aortic syndrome: surgical, endovascular or medical treatment. 15912349 - Tight hamstring syndrome and extra- or intraspinal diseases in childhood: a multicenter... 91669 - Partial klüver-bucy syndrome following probably herpes simplex encephalitis. 19698549 - An epidemiological study on eating disorders in two high schools in naples. 20303099 - Development, validation and testing of an epidemiological case definition of interstiti... 20637399 - Mega aorta syndrome: a case of thoracic and abdominal aortic aneurysm. 8935309 - Double aneuploidy with down's-klinefelter's syndrome. 1307589 - Wildervanck syndrome (cervico-oculo-acoustic syndrome). 15269839 - Association of nos3 gene with metabolic syndrome in hypertensive patients. |
Publication Detail:
|
Type: JOURNAL ARTICLE |
Journal Detail:
|
Title: Orbit (Amsterdam, Netherlands) Volume: 18 ISSN: 1744-5108 ISO Abbreviation: Orbit Publication Date: 1999 Dec |
Date Detail:
|
Created Date: 2002-Jun-4 Completed Date: - Revised Date: - |
Medline Journal Info:
|
Nlm Unique ID: 8301221 Medline TA: Orbit Country: - |
Other Details:
|
Languages: ENG Pagination: 247-259 Citation Subset: - |
Affiliation:
|
Department of Ophthalmology, Ankara Research and Training Hospital, Ankara, Turkey |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
|
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: Use of mitomycin C and 5-fluorouracil in external dacryocystorhinostomy.
Next Document: Thallium-201 SPECT of orbital tumors.