Document Detail


Epidermal nevus syndrome with azygos anterior cerebral artery.
MedLine Citation:
PMID:  18805370     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Epidermal nevus syndrome is a neurocutaneous disorder characterized by the association of epidermal nevi with central nervous system or skeletal abnormalities. Central nervous system abnormalities include hemimegalencephaly, hydrocephalus, various migration disorders, intraspinal lipomas, and enlarged spinal roots. Rarely, vascular anomalies cause neurologic signs. We report on a 30-month-old girl with epidermal nevus syndrome who also exhibited vascular malformations of the azygos anterior cerebral artery, a cortical aneurysm, and right internal carotid artery hypoplasia. This rare vascular abnormality was not previously reported in patients with epidermal nevus syndrome.
Authors:
Bülent Kara; Nagehan Inan; Dilek Bayramgürler; Ozgül Altintaş; Aynur Akbulut
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pediatric neurology     Volume:  39     ISSN:  0887-8994     ISO Abbreviation:  Pediatr. Neurol.     Publication Date:  2008 Oct 
Date Detail:
Created Date:  2008-09-22     Completed Date:  2008-12-02     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8508183     Medline TA:  Pediatr Neurol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  283-5     Citation Subset:  IM    
Affiliation:
Department of Pediatrics, Kocaeli University Faculty of Medicine, Umuttepe, Izmit, Kocaeli, Turkey. bulentkara@excite.com
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / pathology*,  radiography
Anterior Cerebral Artery / abnormalities*
Central Nervous System Vascular Malformations / pathology*
Child, Preschool
Female
Humans
Nevus, Pigmented / pathology*
Skin Neoplasms / pathology*
Syndrome
Tomography, X-Ray Computed / methods

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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