Document Detail


Endosomal TLR signaling is required for anti-nucleic acid and rheumatoid factor autoantibodies in lupus.
MedLine Citation:
PMID:  19574451     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Using the Unc93b1 3d mutation that selectively abolishes nucleic acid-binding Toll-like receptor (TLR) (TLR3, -7, -9) signaling, we show these endosomal TLRs are required for optimal production of IgG autoAbs, IgM rheumatoid factor, and other clinical parameters of disease in 2 lupus strains, B6-Fas(lpr) and BXSB. Strikingly, treatment with lipid A, an autoAb-inducing TLR4 agonist, could not overcome this requirement. The 3d mutation slightly reduced complete Freund's adjuvant (CFA)-mediated antigen presentation, but did not affect T-independent type 1 or alum-mediated T-dependent humoral responses or TLR-independent IFN production induced by cytoplasmic nucleic acids. These findings suggest that nucleic acid-sensing TLRs might act as an Achilles' heel in susceptible individuals by providing a critical pathway by which relative tolerance for nucleic acid-containing antigens is breached and systemic autoimmunity ensues. Importantly, this helps provide an explanation for the high frequency of anti-nucleic acid Abs in lupus-like systemic autoimmunity.
Authors:
Dwight H Kono; M Katarina Haraldsson; Brian R Lawson; K Michael Pollard; Yi Ting Koh; Xin Du; Carrie N Arnold; Roberto Baccala; Gregg J Silverman; Bruce A Beutler; Argyrios N Theofilopoulos
Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural     Date:  2009-07-02
Journal Detail:
Title:  Proceedings of the National Academy of Sciences of the United States of America     Volume:  106     ISSN:  1091-6490     ISO Abbreviation:  Proc. Natl. Acad. Sci. U.S.A.     Publication Date:  2009 Jul 
Date Detail:
Created Date:  2009-07-22     Completed Date:  2009-08-25     Revised Date:  2010-09-27    
Medline Journal Info:
Nlm Unique ID:  7505876     Medline TA:  Proc Natl Acad Sci U S A     Country:  United States    
Other Details:
Languages:  eng     Pagination:  12061-6     Citation Subset:  IM    
Affiliation:
Department of Immunology and Microbial Science, The Scripps Research Institute, La Jolla, CA 92037, USA. dkono@scripps.edu
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MeSH Terms
Descriptor/Qualifier:
Animals
Antibodies, Antinuclear / immunology*
B-Lymphocytes / cytology,  drug effects,  immunology
Dendritic Cells / cytology,  drug effects,  immunology
Endosomes / drug effects,  immunology*
Immunoglobulin G / immunology
Immunoglobulin M / immunology
Lupus Erythematosus, Systemic / immunology*,  pathology
Lymphocyte Activation / drug effects
Male
Mice
Mice, Inbred MRL lpr
Mutation / genetics
Nucleic Acids / pharmacology
Picrates / pharmacology
Rheumatoid Factor / immunology*
Signal Transduction / drug effects,  immunology*
Survival Analysis
T-Lymphocytes / cytology,  drug effects,  immunology
Toll-Like Receptor 4 / immunology
Toll-Like Receptors / immunology*
Grant Support
ID/Acronym/Agency:
AI059777/AI/NIAID NIH HHS; AR053228/AR/NIAMS NIH HHS; AR31203/AR/NIAMS NIH HHS; AR39555/AR/NIAMS NIH HHS; AR42242/AR/NIAMS NIH HHS; ES07511/ES/NIEHS NIH HHS; GM67759/GM/NIGMS NIH HHS
Chemical
Reg. No./Substance:
0/Antibodies, Antinuclear; 0/Immunoglobulin G; 0/Immunoglobulin M; 0/Nucleic Acids; 0/Picrates; 0/Tlr4 protein, mouse; 0/Toll-Like Receptor 4; 0/Toll-Like Receptors; 88-89-1/picric acid; 9009-79-4/Rheumatoid Factor
Comments/Corrections

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