| End-stage cardiac failure caused by isolated ventricular non-compaction: cardiac transplantation in a 5-year-old boy. | |
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MedLine Citation:
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PMID: 15896762 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Isolated ventricular non-compaction (IVNC) is a rare congenital cardiomyopathy characterized by arrest in endomyocardial morphogenesis. Presenting features in children include systolic and diastolic ventricular dysfunction, cardiac arrhythmias, and thromboembolism. End-stage cardiac failure necessitating cardiac transplantation is described in adults. We report the unique case of a 5-year-old boy with IVNC and end-stage heart failure who underwent cardiac transplantation. Diagnostic echocardiographic features, gross cardiac morphology, and histopathologic findings are illustrated. |
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Authors:
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Melanie Vogel; Milind Chaudhari; Doris Rassl; Lara Mair; Asif Hasan |
Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation Volume: 24 ISSN: 1053-2498 ISO Abbreviation: J. Heart Lung Transplant. Publication Date: 2005 May |
Date Detail:
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Created Date: 2005-05-17 Completed Date: 2005-09-20 Revised Date: 2007-11-15 |
Medline Journal Info:
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Nlm Unique ID: 9102703 Medline TA: J Heart Lung Transplant Country: United States |
Other Details:
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Languages: eng Pagination: 618-20 Citation Subset: IM |
Affiliation:
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Department of Paediatric Cardiology Freeman Hospital, Newcastle upon Tyne, United Kingdom. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Cardiomyopathies
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congenital*,
surgery* Child, Preschool Endocardium / abnormalities, embryology Heart / embryology Heart Defects, Congenital / surgery* Heart Failure / etiology, surgery Heart Transplantation* Humans Male Myocardium |
| Comments/Corrections | |
Comment In:
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J Heart Lung Transplant. 2006 Apr;25(4):489
[PMID:
16563984
]
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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