Document Detail


Emerging insights in the management of hemoglobin E beta thalassemia.
MedLine Citation:
PMID:  20712787     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Globally, hemoglobin (Hb) E beta thalassemia accounts for approximately half the severe forms of beta thalassemia. Because of its wide clinical diversity and the ability of patients with this condition to adapt unusually well to low hemoglobin levels, the management of Hb E beta thalassemia, particularly the decision to instigate regular blood transfusion, is particularly difficult. Here, we present a summary of our work in patients with this condition, which attempts to define clinical, adaptive, and genetic factors of possible value in determining the early management of this condition.
Authors:
Nancy F Olivieri; Vivekanandan Thayalsuthan; Angela O'Donnell; Anuja Premawardhena; Christopher Rigobon; Giulia Muraca; Christopher Fisher; David J Weatherall
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Annals of the New York Academy of Sciences     Volume:  1202     ISSN:  1749-6632     ISO Abbreviation:  Ann. N. Y. Acad. Sci.     Publication Date:  2010 Aug 
Date Detail:
Created Date:  2010-08-17     Completed Date:  2010-09-17     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  7506858     Medline TA:  Ann N Y Acad Sci     Country:  United States    
Other Details:
Languages:  eng     Pagination:  155-7     Citation Subset:  IM    
Affiliation:
Hemoglobinopathy Research Program, Toronto General Hospital, University of Toronto, Toronto, Ontario, Canada. noliv@attglobal.net
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MeSH Terms
Descriptor/Qualifier:
Blood Transfusion
Hemoglobin E*
Humans
beta-Thalassemia / physiopathology,  therapy*
Chemical
Reg. No./Substance:
9034-61-1/Hemoglobin E

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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