Document Detail


Elevated fibrinopeptide A (FPA) in patients with Lesch-Nyhan syndrome.
MedLine Citation:
PMID:  1492659     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The detection of elevated fibrinopeptide A (FPA) level in a patient with the Lesch-Nyhan syndrome complicated with cerebral infarction prompted us to examine FPA level in 3 other patients with the syndrome. FPA level significantly increased in all patients. Fibrinopeptide B beta 15-42 (FPB beta 15-42) level was increased in two, and both beta-thromboglobulin (beta TG) and platelet factor 4 (PF4) levels were elevated in one patient. These results suggest coagulation abnormalities in patients with Lesch-Nyhan syndrome.
Authors:
A Imamura; H Yamanouchi; T Kurokawa; M Arima
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Brain & development     Volume:  14     ISSN:  0387-7604     ISO Abbreviation:  Brain Dev.     Publication Date:  1992 Nov 
Date Detail:
Created Date:  1993-03-02     Completed Date:  1993-03-02     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  7909235     Medline TA:  Brain Dev     Country:  JAPAN    
Other Details:
Languages:  eng     Pagination:  424-5     Citation Subset:  IM    
Affiliation:
Division of Child Neurology, National Center Hospital for Mental, Nervous and Muscular Disorders, Tokyo, Japan.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Blood Coagulation Factors / analysis
Child
Fibrinopeptide A / analysis*
Humans
Lesch-Nyhan Syndrome / blood*
Male
Chemical
Reg. No./Substance:
0/Blood Coagulation Factors; 25422-31-5/Fibrinopeptide A

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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