Document Detail


The Ehlers-Danlos syndrome and colonic perforation. Report of a case and physiologic assessment of underlying motility disorder.
MedLine Citation:
PMID:  4064860     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The Ehlers-Danlos syndrome is a genetically determined disorder of connective tissue which is generally known for its features of fragile, hyperextensible skin, hypermobile joints, and tissue fragility. Less commonly, colorectal complications can occur, including bleeding, prolapse, and diverticulitis. A rare case of colonic perforation associated with Ehlers-Danlos syndrome is presented. Additionally, in vitro electromyographic studies of the colonic tissue were performed which suggested a possible link between abnormal myogenic activity and the colonic perforations. The authors recommend that treatment be either a permanent colostomy or a subtotal colectomy with anastomosis to the rectum for similar cases.
Authors:
E Sigurdson; H S Stern; J Houpt; T Y el-Sharkawy; J D Huizinga
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Diseases of the colon and rectum     Volume:  28     ISSN:  0012-3706     ISO Abbreviation:  Dis. Colon Rectum     Publication Date:  1985 Dec 
Date Detail:
Created Date:  1985-12-24     Completed Date:  1985-12-24     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  0372764     Medline TA:  Dis Colon Rectum     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  962-6     Citation Subset:  IM    
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MeSH Terms
Descriptor/Qualifier:
Adult
Colon / physiopathology
Colonic Diseases / etiology*,  physiopathology,  surgery
Ehlers-Danlos Syndrome / complications*
Electromyography
Gastrointestinal Motility*
Humans
Intestinal Perforation / etiology*,  physiopathology,  surgery
Male
Muscle Contraction
Muscle, Smooth / physiopathology

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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