| Ectopic Cushing's syndrome due to an adrenal ganglioneuroma. | |
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MedLine Citation:
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PMID: 20389113 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Background: Cushing's syndrome (CS), rare in children, is due to pituitary or, less frequently, to adrenocortical tumors. Ectopic adrenocorticotropin (ACTH) secretion is exceptional. Method: A case of apparently ACTH-independent CS in a child is reported. Results: CS was due to an adrenal ganglioneuroma where neuroendocrine cells were immunopositive for ACTH responsible for the syndrome through a paracrine effect. Cortical cell hyperplasia was observed. Conclusion: Benign and differentiated tumors of the neural crest such as ganglioneuromas may be responsible for CS. |
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Authors:
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Jean-Benoît Corcuff; Colette Deminiere; Jacqueline Trouillas; Olivier Puel; Yves Perel; Pascal Barat |
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Publication Detail:
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Type: Case Reports; Journal Article Date: 2010-04-14 |
Journal Detail:
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Title: Hormone research in pædiatrics Volume: 73 ISSN: 1663-2826 ISO Abbreviation: Horm Res Paediatr Publication Date: 2010 |
Date Detail:
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Created Date: 2010-04-14 Completed Date: 2010-07-15 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 101525157 Medline TA: Horm Res Paediatr Country: Switzerland |
Other Details:
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Languages: eng Pagination: 405-8 Citation Subset: IM |
Copyright Information:
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Copyright 2010 S. Karger AG, Basel. |
Affiliation:
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Department of Nuclear Medicine, CHU Bordeaux, Bordeaux, France. jean-benoit.corcuff@chu-bordeaux.fr |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Adrenal Cortex Neoplasms / diagnosis, pathology* Adrenal Glands / pathology Adrenocorticotropic Hormone / metabolism Cushing Syndrome / diagnosis, etiology*, pathology Female Ganglioneuroma / diagnosis, pathology* Hormones, Ectopic / metabolism Humans |
| Chemical | |
Reg. No./Substance:
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0/Hormones, Ectopic; 9002-60-2/Adrenocorticotropic Hormone |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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