| Ebstein malformation of the tricuspid valve: current concepts in management and outcomes. | |
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MedLine Citation:
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PMID: 19846038 Owner: NLM Status: In-Data-Review |
Abstract/OtherAbstract:
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Ebstein anomaly is a myopathy of the right ventricle that results in variable degrees of failure of delamination of the tricuspid valve leaflets from the underlying endocardium, leading to severe tricuspid valve regurgitation and some degree of right ventricular dysfunction. In neonates or infants who remain in congestive heart failure or profoundly cyanotic while receiving appropriate medical therapy, operation is required. Current strategies include biventricular or single-ventricle repair. In children and adults, medical management may be used, but most patients eventually require surgery. Tricuspid valve repair is preferred; we believe the cone repair is the most anatomic repair and is the operation of choice. Tricuspid valve replacement may be necessary in cases in which the valve is not repairable. A bidirectional cavopulmonary shunt is useful in patients with severe right ventricular dilatation and/or dysfunction. Transplantation rarely is necessary. |
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Authors:
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Morgan L Brown; Joseph A Dearani |
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Publication Detail:
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Type: Journal Article |
Journal Detail:
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Title: Current treatment options in cardiovascular medicine Volume: 11 ISSN: 1534-3189 ISO Abbreviation: Curr Treat Options Cardiovasc Med Publication Date: 2009 Oct |
Date Detail:
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Created Date: 2009-10-22 Completed Date: - Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 9815942 Medline TA: Curr Treat Options Cardiovasc Med Country: United States |
Other Details:
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Languages: eng Pagination: 396-402 Citation Subset: - |
Affiliation:
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Joseph A. Dearani, MD Division of Cardiovascular Surgery, Mayo Clinic, 200 First Street Southwest, Rochester, MN 55905, USA. jdearani@mayo.edu. |
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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