Document Detail


Early onset methylmalonic aciduria and homocystinuria cblC type with demyelinating neuropathy.
MedLine Citation:
PMID:  20610126     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Methylmalonic aciduria and homocystinuria, cblC type, is the most common inborn error of vitamin B(12) (cobalamin) metabolism. The recent cloning of the disease gene, MMACHC, has permitted genotype-phenotype correlation. In a 1-year-old girl, compound heterozygous c.271dupA and c.616C>T mutations in MMACHC were identified as causing an early onset methylmalonic aciduria and homocystinuria, cblC type, which was complicated by sensorimotor peripheral demyelinating neuropathy.
Authors:
Daniele Frattini; Carlo Fusco; Valentina Ucchino; Barbara Tavazzi; Elvio Della Giustina
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pediatric neurology     Volume:  43     ISSN:  1873-5150     ISO Abbreviation:  Pediatr. Neurol.     Publication Date:  2010 Aug 
Date Detail:
Created Date:  2010-07-08     Completed Date:  2011-01-14     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8508183     Medline TA:  Pediatr Neurol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  135-8     Citation Subset:  IM    
Copyright Information:
Copyright 2010 Elsevier Inc. All rights reserved.
Affiliation:
Child Neurology Unit, Arcispedale Santa Maria Nuova, 42100 Reggio Emilia, Italy. frattini.daniele@asmn.re.it
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MeSH Terms
Descriptor/Qualifier:
Demyelinating Diseases / complications,  urine*
Female
Genetic Association Studies
Homocystinuria / complications,  urine*
Humans
Infant
Methylmalonic Acid / urine*
Neural Conduction / physiology
Peripheral Nervous System Diseases / complications,  urine*
Chemical
Reg. No./Substance:
516-05-2/Methylmalonic Acid

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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