Document Detail


Dominant dorsal duct syndrome: a rare cause of acute recurrent pancreatitis in children revisited.
MedLine Citation:
PMID:  20019564     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Acute recurrent pancreatitis in children can be caused by anomalies of fusion of pancreatic ducts such as the dominant dorsal duct syndrome wherein a dominant dorsal pancreatic duct is associated with stenosis of the minor papilla. Clinical presentations and management of 2 patients are discussed. An infant presented with severe acute pancreatitis with pseudocyst formation due to an underlying ductal disruption. Surgical treatment was offered on account of failure of medical therapy and endoscopic stenting. A dominant dorsal duct with minor papilla stenosis was encountered. Sphincteroplasty of the minor papilla and lateral pancreaticojejunostomy were performed with good result. A 14-year-old boy with a type 1 choledochal cyst was troubled by recurrent acute pancreatitis. At operation, a dilated dorsal pancreatic duct opening into a stenosed minor papilla was found in addition to the choledochal cyst. Choledochal cyst excision, choledochoduodenostomy, and sphincteroplasty of the minor papilla stenosis were performed. Dominant dorsal duct syndrome is a rare cause of acute pancreatitis in children. A high index of suspicion is necessary to establish a precise diagnosis. Sphincteroplasty of the minor papilla may affect adequate pancreatic drainage and prevent recurrent pancreatitis.
Authors:
Aniruddh V Deshpande; Gordon Thomas; Albert Shun; Gerard Roy; Michael Stormon; Kevin Gaskin
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pancreas     Volume:  39     ISSN:  1536-4828     ISO Abbreviation:  Pancreas     Publication Date:  2010 Jan 
Date Detail:
Created Date:  2009-12-18     Completed Date:  2010-04-26     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8608542     Medline TA:  Pancreas     Country:  United States    
Other Details:
Languages:  eng     Pagination:  97-100     Citation Subset:  IM    
Affiliation:
Department of Paediatric Surgery, Children's Hospital at Westmead Sydney, Australia.
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MeSH Terms
Descriptor/Qualifier:
Acute Disease
Adolescent
Choledochal Cyst / diagnosis,  surgery
Humans
Infant
Male
Pancreatic Diseases / complications,  congenital
Pancreatic Ducts / abnormalities*
Pancreatic Pseudocyst / diagnosis,  surgery
Pancreatitis / diagnosis,  etiology,  surgery*
Recurrence
Retrospective Studies
Syndrome
Treatment Outcome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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