Document Detail


Diffuse smooth muscle proliferation of the lungs with severe pulmonary hypertension.
MedLine Citation:
PMID:  8816894     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We describe the second example of a distinctive clinicopathologic syndrome of severe pulmonary hypertension and interstitial lung disease caused by diffuse smooth muscle proliferation of the lungs (DSMPL) occurring in a 44-year-old man of normal intelligence with no cutaneous or neurological lesions. The smooth muscle proliferation involved the walls of bronchioles, alveoli, small pulmonary arteries, and pulmonary veins. DSMPL is distinct from pulmonary lymphangioleiomyomatosis and tuberous sclerosis, and does not appear to be neoplastic or reactive. The lesions are probably best regarded as multiple hamartomas or "native benign nodular smooth muscle proliferations."
Authors:
J M Kay; L M Kahana; C Rihal
Related Documents :
18197144 - Lfa-1 and mac-1 mediate pulmonary recruitment of neutrophils and tissue damage in abdom...
22219424 - Concomitant frozen elephant trunk procedure and pulmonary embolectomy.
1541694 - Increased numbers of pulmonary megakaryocytes in patients with arterial pulmonary tumou...
2477644 - A method for safe twelve-hour pulmonary preservation.
8911404 - Preliminary clinical outcome and imaging criterion for endovascular prosthesis developm...
9806384 - Transatrial-transpulmonary tetralogy of fallot repair is effective in the presence of a...
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Human pathology     Volume:  27     ISSN:  0046-8177     ISO Abbreviation:  Hum. Pathol.     Publication Date:  1996 Sep 
Date Detail:
Created Date:  1996-11-29     Completed Date:  1996-11-29     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  9421547     Medline TA:  Hum Pathol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  969-74     Citation Subset:  IM    
Affiliation:
Department of Pathology, St. Joseph's Hospital, Hamilton Civic Hospitals, Ontario, Canada.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adult
Cell Division
Humans
Hypertension, Pulmonary / pathology*,  physiopathology,  radiography
Lung Diseases, Interstitial / pathology*,  physiopathology,  radiography
Male
Muscle, Smooth / pathology*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Amplification of stromelysin-3 transcripts from carcinomas of the colon.
Next Document:  Primary mediastinal and testicular seminomas: a comparison of K-ras-2 gene sequence and p53 immunope...