Document Detail

Diffuse ganglioneuromatosis in small intestine associated with neurofibromatosis type 1.
MedLine Citation:
PMID:  19118783     Owner:  NLM     Status:  MEDLINE    
Ganglioneuromatosis of the gastrointestinal tract is a rare condition that has an established association with the multiple endocrine neoplasia syndrome, type IIb. Its occurrence in neurofibromatosis, in which the large intestine is usually affected, is much rarer. We report a case of diffuse ganglioneuromatosis of the small bowel, found incidentally during surgery for a malignant peripheral nerve sheath tumor arising in the retroperitoneum in a 32-year-old man with neurofibromatosis type 1, and review previously reported cases.
Khin Thway; Cyril Fisher
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Publication Detail:
Type:  Case Reports; Journal Article; Review     Date:  2007-10-24
Journal Detail:
Title:  Annals of diagnostic pathology     Volume:  13     ISSN:  1532-8198     ISO Abbreviation:  Ann Diagn Pathol     Publication Date:  2009 Feb 
Date Detail:
Created Date:  2009-01-02     Completed Date:  2009-04-03     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9800503     Medline TA:  Ann Diagn Pathol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  50-4     Citation Subset:  IM    
Royal Marsden Hospital, London, United Kingdom.
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MeSH Terms
Fatal Outcome
Ganglioneuroma / pathology*,  surgery
Intestinal Neoplasms / pathology*,  surgery
Neoplasms, Multiple Primary / pathology*,  surgery
Nerve Sheath Neoplasms / pathology*,  surgery
Neurofibromatosis 1 / pathology*,  surgery
Retroperitoneal Neoplasms / pathology*,  surgery

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