Document Detail


Diffuse ganglioneuromatosis in small intestine associated with neurofibromatosis type 1.
MedLine Citation:
PMID:  19118783     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Ganglioneuromatosis of the gastrointestinal tract is a rare condition that has an established association with the multiple endocrine neoplasia syndrome, type IIb. Its occurrence in neurofibromatosis, in which the large intestine is usually affected, is much rarer. We report a case of diffuse ganglioneuromatosis of the small bowel, found incidentally during surgery for a malignant peripheral nerve sheath tumor arising in the retroperitoneum in a 32-year-old man with neurofibromatosis type 1, and review previously reported cases.
Authors:
Khin Thway; Cyril Fisher
Related Documents :
13671363 - Use and abuse of nasogastric intubation.
19568523 - Abdominal cocoon secondary to tuberculosis.
23133083 - Intestinal duplication.
Publication Detail:
Type:  Case Reports; Journal Article; Review     Date:  2007-10-24
Journal Detail:
Title:  Annals of diagnostic pathology     Volume:  13     ISSN:  1532-8198     ISO Abbreviation:  Ann Diagn Pathol     Publication Date:  2009 Feb 
Date Detail:
Created Date:  2009-01-02     Completed Date:  2009-04-03     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9800503     Medline TA:  Ann Diagn Pathol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  50-4     Citation Subset:  IM    
Affiliation:
Royal Marsden Hospital, London, United Kingdom.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adult
Fatal Outcome
Ganglioneuroma / pathology*,  surgery
Humans
Intestinal Neoplasms / pathology*,  surgery
Male
Neoplasms, Multiple Primary / pathology*,  surgery
Nerve Sheath Neoplasms / pathology*,  surgery
Neurofibromatosis 1 / pathology*,  surgery
Retroperitoneal Neoplasms / pathology*,  surgery

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Mantle cell lymphoma in a tubular adenoma: unusual presentation with synchronous colonic carcinoma.
Next Document:  Cerebellar medulloblastoma in the elderly.