Document Detail


Difficulties in anesthetic management of patients with micrognathia: report of a patient with Stickler syndrome.
MedLine Citation:
PMID:  17138163     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Stickler syndrome is an autosomal dominant multisystem disorder with characteristic midface hypoplasia, retromicrognathia, cleft palate and a "moon-shaped" appearance. Progressive myopia and retinal degeneration are frequent. It is estimated that one third of all Pierre Robin patients have Stickler syndrome. Patients with a mandibular hypoplasia like Stickler syndrome present the anesthesiologist considerable problems when mask ventilation or endotracheal intubation is attempted. In this case report the difficulties in anesthetic management of patients with micrognathia and repeated anesthetic courses of a child with Stickler syndrome are presented. It is vital to detect the syndrome in early stages so that adequate counseling and treatment may be given to avoid the potentially irreversible and disabling consequences.
Authors:
Zuhal Küçükyavuz; Ozkan Ozkaynak; Ayşegül Mine Tüzüner; Reha Kişnişçi
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2006-10-02
Journal Detail:
Title:  Oral surgery, oral medicine, oral pathology, oral radiology, and endodontics     Volume:  102     ISSN:  1528-395X     ISO Abbreviation:  Oral Surg Oral Med Oral Pathol Oral Radiol Endod     Publication Date:  2006 Dec 
Date Detail:
Created Date:  2006-12-01     Completed Date:  2006-12-12     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9508562     Medline TA:  Oral Surg Oral Med Oral Pathol Oral Radiol Endod     Country:  United States    
Other Details:
Languages:  eng     Pagination:  e33-6     Citation Subset:  D; IM    
Affiliation:
Ankara University, Faculty of Dentistry, Department of Maxillofacial Surgery, Ankara, Turkey. kucukyavuz65@yahoo.com <kucukyavuz65@yahoo.com>
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MeSH Terms
Descriptor/Qualifier:
Anesthesia, Dental / methods*
Anesthesia, Inhalation / methods*
Anesthetics, Inhalation
Cleft Palate / surgery
Facies
Hearing Loss, Conductive
Humans
Infant
Intubation, Intratracheal / methods*
Male
Mandible / abnormalities*
Methyl Ethers
Micrognathism*
Nitrous Oxide
Syndrome
Chemical
Reg. No./Substance:
0/Anesthetics, Inhalation; 0/Methyl Ethers; 10024-97-2/Nitrous Oxide; 28523-86-6/sevoflurane

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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