| Diaphragm pacers as a treatment for congenital central hypoventilation syndrome. | |
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MedLine Citation:
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PMID: 16293069 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Congenital central hypoventilation syndrome is a rare syndrome present from birth, and is defined as the failure of automatic control of breathing. All patients with congenital central hypoventilation syndrome require life-long ventilatory support during sleep, although approximately a third of patients require ventilatory support 24 h per day. Diaphragm pacers offer a modality of ventilatory support that affords congenital central hypoventilation syndrome patients with maximal mobility for full-time ventilatory patients, and they may allow for a more normal lifestyle in the appropriate patient. They may permit tracheostomy decannulation in those requiring only support during sleep. Diaphragm pacing entails surgical placement of an electrode onto the phrenic nerve, connected to a subcutaneous receiver. There is an external battery-operated transmitter and antenna placed on the skin over the receiver. The transmitter emits energy, similar to radio transmission, which is converted into an electrical current by the receiver. This stimulates the phrenic nerve resulting in a diaphragmatic contraction. Settings on the transmitter include respiratory rate and electrical voltage, and are adjusted to give enough tidal volume to allow for adequate oxygenation and ventilation. Therefore, diaphragm pacing is an attractive alternative mode of mechanically assisted ventilation for many patients with congenital central hypoventilation syndrome. |
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Authors:
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Maida Lynn Chen; Mary Anne Tablizo; Sheila Kun; Thomas G Keens |
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Publication Detail:
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Type: Journal Article; Review |
Journal Detail:
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Title: Expert review of medical devices Volume: 2 ISSN: 1743-4440 ISO Abbreviation: - Publication Date: 2005 Sep |
Date Detail:
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Created Date: 2005-11-18 Completed Date: 2006-01-05 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 101230445 Medline TA: Expert Rev Med Devices Country: England |
Other Details:
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Languages: eng Pagination: 577-85 Citation Subset: IM |
Affiliation:
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University of Southern California, Division of Pediatric Pulmonology, Childrens Hospital Los Angeles, Keck School of Medicine, Los Angeles, CA 90027, USA. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Diaphragm
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innervation,
physiopathology* Electric Stimulation Therapy / instrumentation*, methods Electrodes, Implanted Equipment Design Equipment Failure Analysis Humans Hypoventilation / congenital*, therapy* Pacemaker, Artificial Phrenic Nerve / physiopathology* Sleep Apnea, Central / congenital*, therapy* Telemetry / instrumentation, methods Treatment Outcome |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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