Document Detail


De subitaneis mortibus. X. Familial congential heart block.
MedLine Citation:
PMID:  1112019     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Complete heart block was found shortly after birth in a brother and sister (not twins). Both were treated by electronic pacing because of symptoms attributable to inadequate cardiac output and electrical instability of heart. The boy has done well with his artificial pacemaker and is now six years old. His sister died of complications due in part to the large size of her pacemaker and small size of her body. At necropsy special studies of her heart included the centers for normal impulse formation and concuction. The primary abnormalities were at the junction of atrial septum with atrioventricular (A-V) node, and at the origin of the two bundle branches from the His bundle. The A-V node was isolated by collagen at all its margins except its junction with the His bundle. The proximal His bundle was essentially normal, but from that point on through the initial protions of both the left and right bundle branches there was extensive caseous degeneration which interrupted any possible conduction. These findings are discussed in relation to fetal and postnatal development of the human A-V node, and the His bundle and its branches; and in the context of a recently observed mathematical relationship between sinus rate and two forms of experimentally produced A-V junctional escape rhythms.
Authors:
T N James; R C McKone; A S Hudspeth
Related Documents :
19577039 - Right bundle branch block as a screening test for pulmonary embolism in chronic spinal ...
7967009 - Complete atrioventricular block during left heart catheterization.
15860389 - Effects of right bundle branch block during atrioventricular nodal reentrant tachycardia.
3135619 - The cardiac apex and its superficial blood supply.
7681169 - Rapid resolution of new right bundle branch block in acute anterior myocardial infarcti...
6476549 - Defining electromechanical dissociation.
8737209 - Myocardial contrast echocardiography in acute myocardial infarction. pathophysiological...
8281539 - Cardiac involvement in rheumatoid arthritis: an echocardiographic study.
15009769 - Normalization of coronary fractional flow reserve with successful intracoronary stent p...
Publication Detail:
Type:  Journal Article; Research Support, U.S. Gov't, P.H.S.    
Journal Detail:
Title:  Circulation     Volume:  51     ISSN:  0009-7322     ISO Abbreviation:  Circulation     Publication Date:  1975 Feb 
Date Detail:
Created Date:  1975-05-10     Completed Date:  1975-05-10     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  0147763     Medline TA:  Circulation     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  379-88     Citation Subset:  AIM; IM    
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Atrioventricular Node / pathology,  physiopathology
Autopsy
Bundle of His / pathology,  physiopathology
Cardiac Output
Female
Heart Block / congenital,  genetics*,  therapy
Heart Conduction System / abnormalities*,  pathology,  physiopathology
Heart Defects, Congenital / complications*
Humans
Infant, Newborn
Male
Myocardium / pathology
Necrosis
Organ Size
Pacemaker, Artificial* / adverse effects
Pericarditis / complications,  pathology

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Learned control of blood pressure in patients with high blood pressure.
Next Document:  The deceptive aortic root.