Document Detail


Cystic fibrosis, common variable immunodeficiency and Aspergers syndrome: an immunological and behavioural challenge.
MedLine Citation:
PMID:  19662491     Owner:  NLM     Status:  In-Data-Review    
Abstract/OtherAbstract:
INTRODUCTION: Cystic fibrosis (CF) is of particular importance in Ireland as the Irish population has both the highest incidence (2.98/10,000) and the highest carrier rate (1 in 19) in the world. Primary immunodeficiency has not been previously reported as co-existing with CF.
CASE REPORT: We report a unique case of CF associated with a primary immunodeficiency syndrome-common variable immunodeficiency (CVID).
DISCUSSION: Our patient has CF, CVID and the additional comorbidity of Aspergers syndrome. The challenges inherent in diagnosing and treating such a case are outlined herein and the successful management of this case is evidenced by the well-preserved lung function of our patient.
Authors:
S H Chotirmall; T B Low; T Hassan; P Branagan; C Kernekamp; M G Flynn; C Gunaratnam; N G McElvaney
Publication Detail:
Type:  Journal Article     Date:  2009-08-07
Journal Detail:
Title:  Irish journal of medical science     Volume:  180     ISSN:  1863-4362     ISO Abbreviation:  Ir J Med Sci     Publication Date:  2011 Jun 
Date Detail:
Created Date:  2011-04-21     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  7806864     Medline TA:  Ir J Med Sci     Country:  Ireland    
Other Details:
Languages:  eng     Pagination:  607-9     Citation Subset:  IM    
Affiliation:
Respiratory Research Division, Department of Medicine, Education and Research Centre, Royal College of Surgeons in Ireland, Beaumont Hospital, Beaumont Road, Dublin 9, Republic of Ireland, schotirmall@rcsi.ie.
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