Document Detail


Critical role of CFTR-dependent lipid rafts in cigarette smoke-induced lung epithelial injury.
MedLine Citation:
PMID:  21378025     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Apoptosis of lung epithelial and endothelial cells by exposure to cigarette smoke (CS) severely damages the lung tissue, leading to the pathogenesis of emphysema, but the underlying mechanisms are poorly understood. We have recently established a direct correlation between decreased lipid raft CFTR expression and emphysema progression through increased ceramide accumulation. In the present work, we investigated the role of membrane CFTR in regulating apoptosis and autophagy responses to CS exposure. We report a constitutive and CS-induced increase in the number of TUNEL-positive apoptotic cells in Cftr(-/-) murine lungs compared with Cftr(+/+) murine lungs that also correlated with a concurrent increase in the expression of ceramide, NF-κB, CD95/Fas, lipid raft proteins, and zonula occludens (ZO)-1/2 (P < 0.001). We also verified that stable wild-type CFTR expression in CFBE41o(-) cells controls constitutively elevated caspase-3/7 activity (-1.6-fold, P < 0.001). Our data suggest that membrane CFTR regulates ceramide-enriched lipid raft signaling platforms required for the induction of Fas-mediated apoptotic signaling. In addition, lack of membrane CFTR also modulates autophagy, as demonstrated by the significant increase in constitutive (P < 0.001) and CSE-induced (P < 0.005) perinuclear accumulation of green fluorescent protein-microtubule-associated protein 1 light chain-3 (LC3) in the absence of membrane CFTR (CFBE41o(-) cells). The significant constitutive and CS-induced increase (P < 0.05) in p62 and LC3β expression in CFTR-deficient cells and mice corroborates these findings and suggest a defective autophagy response in the absence of membrane CFTR. Our data demonstrate the critical role of membrane-localized CFTR in regulating apoptotic and autophagic responses in CS-induced lung injury that may be involved in the pathogenesis of severe emphysema.
Authors:
Manish Bodas; Taehong Min; Neeraj Vij
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Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't     Date:  2011-03-04
Journal Detail:
Title:  American journal of physiology. Lung cellular and molecular physiology     Volume:  300     ISSN:  1522-1504     ISO Abbreviation:  Am. J. Physiol. Lung Cell Mol. Physiol.     Publication Date:  2011 Jun 
Date Detail:
Created Date:  2011-06-03     Completed Date:  2011-08-11     Revised Date:  2011-09-26    
Medline Journal Info:
Nlm Unique ID:  100901229     Medline TA:  Am J Physiol Lung Cell Mol Physiol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  L811-20     Citation Subset:  IM    
Affiliation:
Department of Pediatric Respiratory Sciences, The Johns Hopkins University School of Medicine, Baltimore, Maryland, USA.
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MeSH Terms
Descriptor/Qualifier:
Animals
Apoptosis
Autophagy
Blotting, Western
Caspase 3 / metabolism
Caspase 7 / metabolism
Cells, Cultured
Ceramides / metabolism
Cystic Fibrosis Transmembrane Conductance Regulator / metabolism*
Fas Ligand Protein / metabolism
Flow Cytometry
Green Fluorescent Proteins / metabolism
Humans
In Situ Nick-End Labeling
Lung Injury / etiology*,  metabolism,  pathology
Membrane Microdomains / metabolism*
Membrane Proteins / metabolism
Mice
Mice, Inbred CFTR
Mice, Knockout
NF-kappa B / metabolism
Phosphoproteins / metabolism
Smoking / adverse effects*
Grant Support
ID/Acronym/Agency:
R03 HL096931-01/HL/NHLBI NIH HHS; R03 HL096931-02/HL/NHLBI NIH HHS; RHL-096931//PHS HHS; RR-025005/RR/NCRR NIH HHS
Chemical
Reg. No./Substance:
0/Ceramides; 0/Fas Ligand Protein; 0/Membrane Proteins; 0/NF-kappa B; 0/Phosphoproteins; 0/enhanced green fluorescent protein; 0/zonula occludens-1 protein; 0/zonula occludens-2 protein; 126880-72-6/Cystic Fibrosis Transmembrane Conductance Regulator; 147336-22-9/Green Fluorescent Proteins; EC 3.4.22.-/Caspase 3; EC 3.4.22.-/Caspase 7

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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