Document Detail


Cowden's syndrome, Lhermitte-Duclos disease, and sclerotic fibroma.
MedLine Citation:
PMID:  9700384     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The authors report a case of Lhermitte-Duclos disease, or dysplastic cerebellar gangliocytoma, in which a cutaneous sclerotic fibroma was found incidentally during the second resection of a recurrent cerebellar hamartoma. The association of Lhermitte-Duclos disease and sclerotic fibroma with Cowden's syndrome led to a dermatologic examination and confirmation of the diagnosis of Cowden's syndrome. The combination of both Lhermitte-Duclos disease and sclerotic fibroma with Cowden's syndrome has not previously been reported. A review of the 15 cases of Lhermitte-Duclos disease associated with Cowden's syndrome shows no significant gender predilection. Sclerotic fibromas, once thought to be specific for Cowden's syndrome, also are reviewed.
Authors:
M S Chapman; A E Perry; R D Baughman
Related Documents :
9483604 - The alagille's syndrome and its anaesthetic considerations.
11094224 - Large uterine myoma with erythropoietin messenger rna and erythrocytosis.
19364454 - Clinically isolated syndrome and multiple sclerosis: rethinking the arsenal.
15272904 - Flail arm syndrome: a clinical variant of amyotrophic lateral sclerosis.
18335564 - Lethal vascular leak syndrome after denileukin diftitox administration to a patient wit...
8476724 - Human immunodeficiency virus nephropathy.
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  The American Journal of dermatopathology     Volume:  20     ISSN:  0193-1091     ISO Abbreviation:  Am J Dermatopathol     Publication Date:  1998 Aug 
Date Detail:
Created Date:  1998-10-14     Completed Date:  1998-10-14     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  7911005     Medline TA:  Am J Dermatopathol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  413-6     Citation Subset:  IM    
Affiliation:
Department of Medicine, Dartmouth Hitchcock Medical Center, Lebanon, New Hampshire 03756, USA.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adult
Cerebellar Neoplasms / complications,  pathology*
Diagnosis, Differential
Fibroma / complications,  pathology*
Ganglioneuroma / complications,  pathology*
Hamartoma Syndrome, Multiple / complications,  pathology*
Humans
Male
Skin Diseases / complications,  pathology*
Skin Neoplasms / complications,  pathology*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Malignant blue nevus of the vulva with late ovarian metastasis.
Next Document:  "Aleukemic" granulomatous leukemia cutis.