Document Detail


Corneal ulceration due to vitamin A deficiency in Zellweger syndrome.
MedLine Citation:
PMID:  19541270     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report a case of vitamin A deficiency and secondary corneal ulcer in an infant with Zellweger syndrome. A 7-month-old infant with failure to thrive and malnutrition developed a corneal ulcer. Fortified antibiotic eye drops were administered without improvement. Vitamin A deficiency was suspected and confirmed. Supplementation with oral vitamin A decreased corneal opacification. Zellweger syndrome was later diagnosed. Vitamin A deficiency should be considered in the differential diagnosis of nonhealing corneal ulcers in children, especially those with systemic syndromes and failure to thrive.
Authors:
Jeffrey D Colburn; Anna S Skelo; Sean P Donahue
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of AAPOS : the official publication of the American Association for Pediatric Ophthalmology and Strabismus / American Association for Pediatric Ophthalmology and Strabismus     Volume:  13     ISSN:  1528-3933     ISO Abbreviation:  J AAPOS     Publication Date:  2009 Jun 
Date Detail:
Created Date:  2009-06-22     Completed Date:  2009-09-21     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9710011     Medline TA:  J AAPOS     Country:  United States    
Other Details:
Languages:  eng     Pagination:  289-91     Citation Subset:  IM    
Affiliation:
Vanderbilt University Medical Center, Nashville, Tennessee 37232, USA.
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MeSH Terms
Descriptor/Qualifier:
Administration, Oral
Corneal Ulcer / diagnosis,  etiology*
Diagnosis, Differential
Female
Humans
Infant
Vitamin A / administration & dosage
Vitamin A Deficiency / complications*,  diagnosis,  drug therapy
Vitamins / administration & dosage
Zellweger Syndrome / complications*,  diagnosis
Chemical
Reg. No./Substance:
0/Vitamins; 11103-57-4/Vitamin A

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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