Document Detail

Congenital ring-constriction syndrome of the limbs; a report of 19 cases.
MedLine Citation:
PMID:  3382854     Owner:  NLM     Status:  MEDLINE    
The authors report 19 cases of congenital ring-constriction syndrome of the limbs. Complications arose in eight of the pregnancies. The limb anomalies were always congenital ring-constrictions together with distal amputation. Moreover, 13 patients also had syndactyly and 15 associated anomalies were registered in 9 patients--8 of the limbs, 3 craniofacial and 4 visceral. One patient had a family history of hypospadias and cardiac malformation. Treatment usually required several operations, staged Z-plasty being the procedure of choice in surgical release of constriction bands. The acrosyndactylies were released early in life. More extensive fusions required division and skin grafting even if the webs did exist. The aetiology of the condition is still under discussion. The number of cases in the literature that cannot be explained by the exogenous theory of the congenital ring-constriction syndrome is increasing. Among them are four cases in our series.
D Rossillon; J J Rombouts; C Verellen-Dumoulin; R Vanwijck; A Vincent; A de Coninck
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  British journal of plastic surgery     Volume:  41     ISSN:  0007-1226     ISO Abbreviation:  Br J Plast Surg     Publication Date:  1988 May 
Date Detail:
Created Date:  1988-08-11     Completed Date:  1988-08-11     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  2984714R     Medline TA:  Br J Plast Surg     Country:  SCOTLAND    
Other Details:
Languages:  eng     Pagination:  270-7     Citation Subset:  IM    
Department of Plastic Surgery, St Luc Hospital, Catholic University of Louvain, Brussels, Belgium.
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MeSH Terms
Abnormalities, Multiple / pathology,  surgery*
Child, Preschool
Constriction, Pathologic / congenital,  pathology
Extremities / pathology
Limb Deformities, Congenital*
Surgery, Plastic*

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