Document Detail


Congenital onychodysplasia of the index fingers--Iso-Kikuchi syndrome. A case involving the second toenail.
MedLine Citation:
PMID:  9167348     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report a case of congenital onychodysplasia of the index fingers (Iso-Kikuchi syndrome) in a 2-year-old boy who had nail deformities on both index fingers and the left second toe. He had a micronychia of the left index fingernail, malalignment and abnormal lunula of the right index fingernail and micronychia and malalignment of the left second toenail. Congenital onychodysplasia of the index fingers (COIF) is a rare condition characterized by various forms of nail dysplasia commonly involving the index fingers, but not infrequently also the neighbouring fingers such as the middle fingers and thumbs. The five criteria characterizing COIF include the following: (i) congenital occurrence; (ii) unilateral or bilateral index finger involvement; (iii) variability in nail appearance; (iv)possible hereditary involvement; and (v) frequently associated bone abnormalities. The nails of COIF include the full spectrum of nail dysplasia, from an irregular lunula, malalignment, micronychia (hypoplastic and rudimental), polyonychia (split rudimental), and anonychia, specifically affecting the index fingers. Our patient represents various forms of nail dysplasia of the both index fingers and left second toe such as micronychia, malalignment and abnormal lunula. To our knowledge, the association with second toenail dysplasia in COIF has not previously been reported.
Authors:
S H Youn; O S Kwon; K C Park; J I Youn; J H Chung
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Clinical and experimental dermatology     Volume:  21     ISSN:  0307-6938     ISO Abbreviation:  Clin. Exp. Dermatol.     Publication Date:  1996 Nov 
Date Detail:
Created Date:  1997-06-17     Completed Date:  1997-06-17     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  7606847     Medline TA:  Clin Exp Dermatol     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  457-8     Citation Subset:  IM    
Affiliation:
Department of Dermatology, Seoul National University College of Medicine, Korea.
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MeSH Terms
Descriptor/Qualifier:
Child, Preschool
Fingers
Humans
Male
Nails / pathology
Nails, Malformed / congenital*,  pathology
Toes

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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