Document Detail


Congenital neutropenia syndromes.
MedLine Citation:
PMID:  18424332     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Congenital neutropenia syndromes comprise a heterogeneous group of inherited disorders. Hereditary conditions associated with low neutrophil counts are persistent and need to be differentiated from neutropenia secondary to autoimmune processes or other pathologic conditions, such as myelodysplasia or leukemia. Clinically, congenital neutropenia is characterized by recurrent bacterial infections. Recently, several novel genetic defects were described in patients with congenital neutropenia, shedding light on the pathophysiology of these rare diseases.
Authors:
Kaan Boztug; Karl Welte; Cornelia Zeidler; Christoph Klein
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't; Review    
Journal Detail:
Title:  Immunology and allergy clinics of North America     Volume:  28     ISSN:  0889-8561     ISO Abbreviation:  Immunol Allergy Clin North Am     Publication Date:  2008 May 
Date Detail:
Created Date:  2008-04-21     Completed Date:  2008-08-12     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8805635     Medline TA:  Immunol Allergy Clin North Am     Country:  United States    
Other Details:
Languages:  eng     Pagination:  259-75, vii-viii     Citation Subset:  IM    
Affiliation:
Department of Pediatric Hematology/Oncology, Medical School Hannover, Carl-Neuberg-Strasse 1, D-30625 Hannover, Germany.
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MeSH Terms
Descriptor/Qualifier:
Humans
Hypopigmentation* / immunology
Leukemia / etiology*,  genetics,  immunology,  metabolism
Neutropenia / congenital*,  diagnosis,  genetics,  physiopathology
Prognosis
Risk Factors
Syndrome

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