| Congenital nephrotic syndrome: report of an infant with diffuse mesangial sclerosis. | |
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MedLine Citation:
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PMID: 14964988 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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A case of congenital nephrotic syndrome (CNS) caused by diffuse mesangial sclerosis (DMS) is presented. A female baby weighting 2,680 gm was delivered at 35 weeks' gestation. She had early onset of generalized edema, heavy proteinuria, oligouria, uncorrectable hypoalbuminemia, and rapid progression to renal failure. Even after being treated with strong antibiotics (teicoplanin and ceftazidine), the infant died of septic shock with Enterobacter cloacea, only sensitive to imipenem, at the age of 7 days. The necropsy showed diffuse mesangial sclerosis. This case demonstrates that prematurity, low birth body weight and early onset of symptoms are not pathognomonic of the congenital nephrotic syndrome of the Finnish type (CNF). It can also occur in DMS. Besides, empirical antibiotics should be started promptly and should cover the major hospital strains of bacteria if the patient is not well. |
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Authors:
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Jei-Wen Chang; Ling-Yu Yang |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Acta paediatrica Taiwanica = Taiwan er ke yi xue hui za zhi Volume: 44 ISSN: 1608-8115 ISO Abbreviation: Acta Paediatr Taiwan Publication Date: 2003 Sep-Oct |
Date Detail:
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Created Date: 2004-02-13 Completed Date: 2004-04-08 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 100958202 Medline TA: Acta Paediatr Taiwan Country: China (Republic: 1949- ) |
Other Details:
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Languages: eng Pagination: 300-2 Citation Subset: IM |
Affiliation:
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Department of Pediatrics of Veteran General Hospital, National Yang-Ming University, Taipei, Taiwan. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Female Glomerular Mesangium / pathology* Humans Infant, Newborn Nephrotic Syndrome / congenital*, pathology Sclerosis |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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