| Congenital cystic adenomatoid malformation connected to an extralobar pulmonary sequestration in the contralateral chest: common origin? | |
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MedLine Citation:
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PMID: 15300558 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Extralobar pulmonary sequestration (ELS) and congenital cystic adenomatoid malformation have been reported to coexist in several variations. This suggests a common embryologic origin. A 6-month-old boy presented with a history of recurrent pneumonias. The patient was diagnosed with a right lower lobe congenital cystic adenomatoid malformation (CCAM) and a left lower lobe ELS/CCAM. The diagnosis was made with the aid of a multidetector computed tomography (CT). Three-dimensional CT reconstruction showed the presence of a right lower lobe CCAM, a left lower ELS with an aberrant arterial supply from the celiac axis, and possible venous drainage into the right CCAM. The patient underwent a right thoracotomy. Intraoperatively, the lesions were discovered to be connected by a band of tissue. The right lower lobe CCAM and the left ELS were removed from the right chest. Histologic analysis confirmed the presence of a CCAM within the right lower lobe. The ELS had involvement of a type II CCAM within the sequestration. The connection between the right CCAM and left ELS/CCAM showed an anomalous conducting airway, anomalous vein, and anomalous artery connecting the 2 lesions. The authors present the first case of a CCAM connected to an ELS/CCAM in the contralateral hemithorax. The unique anatomic configuration of these lesions suggests a common embryologic origin of ELS and CCAM. |
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Authors:
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Sean E McLean; John D Pfeifer; Marilyn J Siegel; Eric R Jensen; Pamela M Schuler; Russel Hirsch; George B Mychaliska |
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Publication Detail:
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Type: Case Reports; Journal Article; Review |
Journal Detail:
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Title: Journal of pediatric surgery Volume: 39 ISSN: 1531-5037 ISO Abbreviation: J. Pediatr. Surg. Publication Date: 2004 Aug |
Date Detail:
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Created Date: 2004-08-09 Completed Date: 2005-04-14 Revised Date: 2005-11-16 |
Medline Journal Info:
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Nlm Unique ID: 0052631 Medline TA: J Pediatr Surg Country: United States |
Other Details:
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Languages: eng Pagination: e13-7 Citation Subset: IM |
Affiliation:
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Department of Surgery, Washington University School of Medicine, St Louis, MO, USA. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Bronchopulmonary Sequestration
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embryology*,
radiography,
surgery Cystic Adenomatoid Malformation of Lung, Congenital / embryology*, radiography, surgery Humans Imaging, Three-Dimensional Infant Infant, Newborn Lung / blood supply, embryology Male Mesoderm / physiology Models, Biological Pneumonia / etiology Recurrence Respiratory Distress Syndrome, Newborn / etiology Thoracotomy Tomography, Spiral Computed |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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