Document Detail


Congenital cataract, microphthalmia and septal heart defect in two generations: a new syndrome?
MedLine Citation:
PMID:  8281271     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The association of congenital cataracts, microphthalmia and heart disease is well recognized in fetal rubella, but genetic causes are comparatively rare and recurrence risks are usually low. We describe a woman with an atrial septal defect, bilateral congenital cataracts, unilateral microphthalmia and minor dysmorphic features, originally attributed to an unidentified infection in utero, whose daughter has a similar constellation of heart, eye and facial abnormalities. This may represent a new dominantly inherited syndrome.
Authors:
A O Wilkie; D Taylor; P J Scambler; M Baraitser
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Clinical dysmorphology     Volume:  2     ISSN:  0962-8827     ISO Abbreviation:  Clin. Dysmorphol.     Publication Date:  1993 Apr 
Date Detail:
Created Date:  1994-02-17     Completed Date:  1994-02-17     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  9207893     Medline TA:  Clin Dysmorphol     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  114-9     Citation Subset:  IM    
Affiliation:
Department of Paediatric Genetics, Hospital for Sick Children, London, UK.
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / genetics*
Adult
Cataract / congenital*
Face / abnormalities
Female
Heart Septal Defects / genetics*
Humans
Infant
Microphthalmos / genetics*
Syndrome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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