Document Detail


Congenital analbuminaemia: biochemical and clinical implications. A case report and literature review.
MedLine Citation:
PMID:  15300429     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Congenital analbuminaemia was diagnosed in a small-for-gestational-age neonate presenting with placental and body oedema, an unusual presentation of this rare autosomal recessive disorder. A review of 39 reported cases in the literature shows that the clinical symptoms are always remarkably mild and that the diagnosis is rarely made in infancy. The absence of albumin appears to be partly counterbalanced by high levels of non-albumin proteins and circulatory adaptations. However, congenital analbuminemia can have important complications: lipodystrophy and hypercholesterolaemia, possibly leading to atherosclerosis. Other possible complications reported in literature are hypercoagulability, osteoporosis, respiratory tract infections, intrauterine growth retardation and intrauterine death. Moreover, albumin-binding drugs should be used with caution. CONCLUSION: Congenital analbuminaemia is a rare disorder with remarkably mild signs and symptoms at all ages. Although often thought to be innocent, this disorder may have important clinical complications.
Authors:
Bart G P Koot; Roderick Houwen; Dirk-Jan Pot; Jeroen Nauta
Related Documents :
2802459 - External and middle ear malformations: autosomal dominant genetic transmission.
16498629 - Distal 4p microdeletion in a case of wolf-hirschhorn syndrome with congenital diaphragm...
15141319 - Anorectal malformation with congenital absence of vagina: a case report and review of t...
19337779 - Malformations of the midbrain and hindbrain: a retrospective study and review of the li...
20647939 - Congenital unilateral absence of sternocleidomastoid and trapezius muscles: a case repo...
23422579 - An unusual case of neonatal cholestasis.
7650239 - Immunoglobulins specific to mosquito salivary gland proteins in the sera of persons wit...
2247379 - Histoplasmosis duboisii (african histoplasmosis). an african case reported from chile w...
2802459 - External and middle ear malformations: autosomal dominant genetic transmission.
Publication Detail:
Type:  Case Reports; Journal Article; Review     Date:  2004-08-06
Journal Detail:
Title:  European journal of pediatrics     Volume:  163     ISSN:  0340-6199     ISO Abbreviation:  Eur. J. Pediatr.     Publication Date:  2004 Nov 
Date Detail:
Created Date:  2004-10-25     Completed Date:  2005-03-01     Revised Date:  2005-11-16    
Medline Journal Info:
Nlm Unique ID:  7603873     Medline TA:  Eur J Pediatr     Country:  Germany    
Other Details:
Languages:  eng     Pagination:  664-70     Citation Subset:  IM    
Affiliation:
Department of Paediatrics, St. Franciscus Gasthuis and Erasmus MC, Sophia Children's Hospital, Rotterdam, The Netherlands, b.g.koot@amc.uva.nl
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adult
Chorionic Villi / pathology*
Edema / genetics*
Female
Humans
Infant, Newborn
Infant, Small for Gestational Age
Placenta / pathology*
Serum Albumin / analysis,  deficiency*,  genetics
Chemical
Reg. No./Substance:
0/Serum Albumin

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Chemotherapeutic management of recurrent/metastatic uterine carcinosarcomas (malignant mixed mulleri...
Next Document:  Primary sternal osteomyelitis due to community-associated methicillin-resistant Staphylococcus aureu...