Document Detail


Congenital adrenal hyperplasias.
MedLine Citation:
PMID:  11469809     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Congenital adrenal hyperplasia syndromes result from deficiencies of enzymes involved in corticosteroid biosynthesis. Most commonly, they are due to mutations in 21-hydroxylase. This chapter describes the clinical diagnosis and management of congenital adrenal hyperplasias throughout life, including in the fetus, child and adult. These clinical recommendations are explained in the context of the molecular and biochemical characteristics of the diseases.
Authors:
P C White
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Publication Detail:
Type:  Journal Article; Research Support, U.S. Gov't, P.H.S.; Review    
Journal Detail:
Title:  Best practice & research. Clinical endocrinology & metabolism     Volume:  15     ISSN:  1521-690X     ISO Abbreviation:  Best Pract. Res. Clin. Endocrinol. Metab.     Publication Date:  2001 Mar 
Date Detail:
Created Date:  2001-07-25     Completed Date:  2001-08-16     Revised Date:  2007-11-14    
Medline Journal Info:
Nlm Unique ID:  101120682     Medline TA:  Best Pract Res Clin Endocrinol Metab     Country:  England    
Other Details:
Languages:  eng     Pagination:  17-41     Citation Subset:  IM    
Affiliation:
Division of Pediatric Endocrinology, UT Southwestern Medical Center, Dallas, TX 75235-9063, USA.
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MeSH Terms
Descriptor/Qualifier:
Adrenal Hyperplasia, Congenital / complications,  diagnosis*,  genetics,  therapy*
Humans
Molecular Biology
Mutation
Grant Support
ID/Acronym/Agency:
R37DK37 867/DK/NIDDK NIH HHS

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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