Document Detail

Congenital absence of the portal vein associated with focal nodular hyperplasia of the liver and cystic dysplasia of the kidney.
MedLine Citation:
PMID:  9578962     Owner:  NLM     Status:  MEDLINE    
Congenital absence of portal vein is a rare malformation. To date, 16 cases have been reported--all in association with other anomalies, i.e. benign or malignant hepatic neoplasms in 6 cases and cardiac malformations in 12. This case report described a girl with congenital absence of portal vein, focal nodular hyperplasia of the liver and cystic kidney dysplasia. Angiography showed the splenic vein and superior mesenteric vein joining to form a common trunk that entered the inferior vena cava directly above the liver. A review of the other cases in the literature is provided and the clinical aspects of our patient are discussed.
G Guariso; S Fiorio; G Altavilla; P G Gamba; T Toffolutti; M Chiesura-Corona; U Tedeschi; L Zancan
Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  European journal of pediatrics     Volume:  157     ISSN:  0340-6199     ISO Abbreviation:  Eur. J. Pediatr.     Publication Date:  1998 Apr 
Date Detail:
Created Date:  1998-07-16     Completed Date:  1998-07-16     Revised Date:  2005-11-16    
Medline Journal Info:
Nlm Unique ID:  7603873     Medline TA:  Eur J Pediatr     Country:  GERMANY    
Other Details:
Languages:  eng     Pagination:  287-90     Citation Subset:  IM    
Department of Pediatrics, University of Padova, Italy.
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MeSH Terms
Cell Division / physiology
Liver / abnormalities*,  pathology
Liver Regeneration / physiology
Polycystic Kidney Diseases / congenital*,  pathology
Portal Vein / abnormalities*,  pathology

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