Document Detail


Congenital absence of the portal vein associated with focal nodular hyperplasia of the liver and cystic dysplasia of the kidney.
MedLine Citation:
PMID:  9578962     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Congenital absence of portal vein is a rare malformation. To date, 16 cases have been reported--all in association with other anomalies, i.e. benign or malignant hepatic neoplasms in 6 cases and cardiac malformations in 12. This case report described a girl with congenital absence of portal vein, focal nodular hyperplasia of the liver and cystic kidney dysplasia. Angiography showed the splenic vein and superior mesenteric vein joining to form a common trunk that entered the inferior vena cava directly above the liver. A review of the other cases in the literature is provided and the clinical aspects of our patient are discussed.
Authors:
G Guariso; S Fiorio; G Altavilla; P G Gamba; T Toffolutti; M Chiesura-Corona; U Tedeschi; L Zancan
Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  European journal of pediatrics     Volume:  157     ISSN:  0340-6199     ISO Abbreviation:  Eur. J. Pediatr.     Publication Date:  1998 Apr 
Date Detail:
Created Date:  1998-07-16     Completed Date:  1998-07-16     Revised Date:  2005-11-16    
Medline Journal Info:
Nlm Unique ID:  7603873     Medline TA:  Eur J Pediatr     Country:  GERMANY    
Other Details:
Languages:  eng     Pagination:  287-90     Citation Subset:  IM    
Affiliation:
Department of Pediatrics, University of Padova, Italy.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Cell Division / physiology
Child
Female
Humans
Hyperplasia
Liver / abnormalities*,  pathology
Liver Regeneration / physiology
Polycystic Kidney Diseases / congenital*,  pathology
Portal Vein / abnormalities*,  pathology

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Faecal immunoreactive lipase: a simple diagnostic test for cystic fibrosis.
Next Document:  Epstein-Barr virus DNA in the cerebrospinal fluid of an HIV patient with primary cerebral lymphoma.