| Congenital immature teratoma mimicking Cushing's disease. | |
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MedLine Citation:
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PMID: 20516739 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Cushing's disease in a neonate is rare and has been reported secondary to pituitary macroadenoma. A case of Cushing's syndrome due to congenital immature teratoma in the region of the pituitary has never been reported. We discuss a case of a neonate who presented with Cushing's syndrome secondary to a congenital immature teratoma in sellar, suprasellar and parasellar regions with ectopic ACTH secretion, thereby mimicking Cushing's disease. The management issues and prognosis of congenital teratomas and neonatal Cushing's syndrome have been discussed. We describe the first case of intracranial ectopic ACTH secreting teratoma in a young infant. The prognosis is usually bad unless total excision is achieved. In the preoperative period and in case of subtotal excision, chemotherapy to take care of hypercortisolemia may be given. |
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Authors:
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Pravin Salunke; Anil Bhansali; Pinnaki Dutta; Arun Bansal; Kirti Gupta; Rakesh K Vasishta; Paramjeet Singh; Kanchan K Mukherjee |
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Publication Detail:
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Type: Case Reports; Journal Article Date: 2010-05-27 |
Journal Detail:
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Title: Pediatric neurosurgery Volume: 46 ISSN: 1423-0305 ISO Abbreviation: Pediatr Neurosurg Publication Date: 2010 |
Date Detail:
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Created Date: 2010-06-16 Completed Date: 2010-09-22 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 9114967 Medline TA: Pediatr Neurosurg Country: Switzerland |
Other Details:
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Languages: eng Pagination: 46-50 Citation Subset: IM |
Copyright Information:
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Copyright 2010 S. Karger AG, Basel. |
Affiliation:
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Department of Neurosurgery, Postgraduate Institute of Medical Education and Research, Chandigarh, India. drpravin_salunke@yahoo.co.uk |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adrenocorticotropic Hormone
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secretion Biopsy Brain Neoplasms / complications*, congenital, pathology*, surgery Fatal Outcome Female Humans Infant Magnetic Resonance Imaging Pituitary ACTH Hypersecretion / etiology*, pathology* Sella Turcica / pathology Teratoma / complications*, congenital, pathology*, surgery |
| Chemical | |
Reg. No./Substance:
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9002-60-2/Adrenocorticotropic Hormone |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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