| Compliance of the diet restricted with leucine, isoleucine and valine in maple syrup urine disease (MSUD) children | |
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MedLine Citation:
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PMID: 17711097 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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The aim of this study was to evaluate the compliance of the diet with limited branched-chain amino acids (BCAA) content in long-term observation of patients with maple syrup urine disease (MSUD). The study group consisted of 7 children at age of 1.5-18 years. Nutrition evaluation was based on current diet records from 3-4 days, every 3-4 months. Energy and nutrition values of proposed daily products lists and diet records was compared with adequate references and recommendations. Energy and content of most of the nutrients in proposed daily products lists were in agreement with RDI except calcium. Diet analysis at MSUD children revealed insufficient contents of: iron, zinc, copper, vitamin B1, B2, niacin and vitamin C (often below 90% RDI). |
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Authors:
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Agnieszka Kowalik; Lucyna Narojek; Jolanta Sykut-Cegielska |
Publication Detail:
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Type: English Abstract; Journal Article |
Journal Detail:
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Title: Roczniki Państwowego Zakładu Higieny Volume: 58 ISSN: 0035-7715 ISO Abbreviation: Rocz Panstw Zakl Hig Publication Date: 2007 |
Date Detail:
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Created Date: 2007-08-22 Completed Date: 2008-01-10 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 0414756 Medline TA: Rocz Panstw Zakl Hig Country: Poland |
Other Details:
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Languages: pol Pagination: 95-101 Citation Subset: IM |
Affiliation:
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Poradnia Zywieniowa, Klinika Pediatrii Instytut Pomnik-Centrum Zdrowia Dziecka, 04-730 Warszawa. kowalikagnieszka@op.pl |
Vernacular Title:
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Realizacja diety z ograniczeniem leucyny, izoleucyny i waliny u dzieci z choroba syropu klonowego (MSUD). |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Calcium / deficiency Child Child, Preschool Copper / deficiency Diet Records Dietary Proteins / metabolism Energy Intake Female Humans Infant Iron / deficiency Isoleucine / administration & dosage, metabolism* Leucine / administration & dosage, metabolism* Longitudinal Studies Male Maple Syrup Urine Disease / diet therapy*, metabolism* Nutritional Requirements Patient Compliance / statistics & numerical data* Valine / administration & dosage, metabolism* Vitamins / administration & dosage Zinc / deficiency |
| Chemical | |
Reg. No./Substance:
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0/Dietary Proteins; 0/Vitamins; 61-90-5/Leucine; 7004-03-7/Valine; 73-32-5/Isoleucine; 7439-89-6/Iron; 7440-50-8/Copper; 7440-66-6/Zinc; 7440-70-2/Calcium |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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