Document Detail

Common pulmonary vein atresia: the role of extracorporeal membrane oxygenation.
MedLine Citation:
PMID:  8424018     Owner:  NLM     Status:  MEDLINE    
Common pulmonary vein atresia is a rare form of cyanotic congenital heart disease in which the pulmonary veins join to form a blind confluence that does not communicate with the heart or the major systemic veins. Twenty-one cases have been reported since the lesion was first described in 1962; only two patients with this lesion have survived. Over a 4-year period, common pulmonary vein atresia was diagnosed in five newborns referred to the San Diego Regional Extracorporeal Membrane Oxygenation Program. All five improved dramatically as a result of venoarterial bypass. Congenital heart disease was diagnosed at autopsy in the initial case and by cardiac ultrasound and/or catheterization in the others. Surgical repair was attempted in three neonates; all three required continued extracorporeal membrane oxygenation support postoperatively because of pulmonary hypertension and severe pulmonary parenchymal disease. One infant died of respiratory insufficiency at 3 months of age. The other two survived and were discharged from the hospital. The diagnostic and therapeutic dilemmas posed by this lesion and the life-saving potential for extracorporeal membrane oxygenation in this rapidly fatal cardiac anomaly are the bases of this report.
G G Dudell; M L Evans; H F Krous; R L Spicer; J J Lamberti
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Pediatrics     Volume:  91     ISSN:  0031-4005     ISO Abbreviation:  Pediatrics     Publication Date:  1993 Feb 
Date Detail:
Created Date:  1993-02-25     Completed Date:  1993-02-25     Revised Date:  2007-11-15    
Medline Journal Info:
Nlm Unique ID:  0376422     Medline TA:  Pediatrics     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  403-10     Citation Subset:  AIM; IM    
Division of Neonatology, Children's Hospital, San Diego, CA 92123.
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MeSH Terms
Apgar Score
Blood Gas Analysis
California / epidemiology
Cardiac Surgical Procedures
Congenital Abnormalities / diagnosis,  epidemiology,  therapy*
Diagnosis, Differential
Extracorporeal Membrane Oxygenation / methods,  standards*
Follow-Up Studies
Heart Catheterization
Hospitals, Pediatric
Hospitals, University
Infant, Newborn
Pulmonary Veins / abnormalities*
Referral and Consultation
Survival Rate
Treatment Outcome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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