Document Detail


Combination of apolipoprotein E2 and lipoprotein lipase heterozygosity causes severe hypertriglyceridemia during pregnancy.
MedLine Citation:
PMID:  16142021     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Pregnancy is a physiological condition where plasma triglyceride levels are moderately increased. This results from raised synthesis of very-low-density lipoproteins (VLDL) in response to elevated estrogen levels. The occurrence of marked hypertriglyceridemia (HTG) is rare and may result from combination of heterozygote mutation in the lipoprotein lipase (LPL) gene and apolipoprotein E2 isoform, as reported in this case. This observation illustrates the interaction between genetic and environmental factors, since pregnancy may disclose a silent LPL deficiency. The risk of acute pancreatitis threatens both the mother and fetus lives. Early recognition of severe HTG and appropriate management are essential for a successful pregnancy outcome.
Authors:
S Hiéronimus; P Benlian; P Bayer; A Bongain; A Fredenrich
Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Diabetes & metabolism     Volume:  31     ISSN:  1262-3636     ISO Abbreviation:  Diabetes Metab.     Publication Date:  2005 Jun 
Date Detail:
Created Date:  2005-09-05     Completed Date:  2005-09-21     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  9607599     Medline TA:  Diabetes Metab     Country:  France    
Other Details:
Languages:  eng     Pagination:  295-7     Citation Subset:  IM    
Affiliation:
Service d'endocrinologie-médecine de la reproduction, Hôpital l'Archet, Nice, France. Hieronimus.s@chu-nice.fr
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MeSH Terms
Descriptor/Qualifier:
Apolipoprotein E2
Apolipoproteins E / genetics*
Female
Heterozygote Detection*
Humans
Hypertriglyceridemia / genetics*
Lipoprotein Lipase / genetics*
Mutation
Pregnancy
Pregnancy Complications / blood*
Chemical
Reg. No./Substance:
0/Apolipoprotein E2; 0/Apolipoproteins E; EC 3.1.1.34/Lipoprotein Lipase

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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