Document Detail


Coding region of IRF6 gene may not be causal for Van der Woude syndrome in cases from India.
MedLine Citation:
PMID:  19929101     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
OBJECTIVE: Evaluation of the IRF6 gene in Van der Woude syndrome cases from an Indian population. SUBJECTS: Nine affected and four unaffected individuals from seven families with Van der Woude syndrome as well as five normal controls (with no history of Van der Woude or any other congenital malformation and belonging to the same geographical area as the families with Van der Woude syndrome). METHOD: Direct sequencing of all coding regions and exon-intron boundaries of the IRF6 gene. RESULTS: Five novel variants: IVS1+3900 A>G, 191 T>C, IVS4+775 C>T, IVS8+218 C>T, 1511 T>A (Ser 416 Arg) and two known variants: IVS6+27 C>G, 1083 G>A (V274I) were detected. Except for one, all were in noncoding regions either in 3'UTR or in introns. There was only one mutation in the coding region, detected in a normal control. CONCLUSION: The present report indicates that point mutations in the coding region of the IRF6 gene may not be a major cause of Van der Woude syndrome in Indian populations.
Authors:
Akhtar Ali; Subodh Kumar Singh; Rajiva Raman
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't     Date:  2009-03-02
Journal Detail:
Title:  The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association     Volume:  46     ISSN:  1055-6656     ISO Abbreviation:  Cleft Palate Craniofac. J.     Publication Date:  2009 Sep 
Date Detail:
Created Date:  2009-11-25     Completed Date:  2010-01-27     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9102566     Medline TA:  Cleft Palate Craniofac J     Country:  United States    
Other Details:
Languages:  eng     Pagination:  541-4     Citation Subset:  D; IM    
Affiliation:
Department of Zoology, Banaras Hindu University, Varanasi, India.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
3' Untranslated Regions / genetics
Abnormalities, Multiple / genetics
Adenine
Arginine / genetics
Cleft Lip / genetics*
Cleft Palate / genetics*
Cohort Studies
Cytosine
Exons / genetics
Female
Genetic Variation / genetics
Genotype
Guanine
Heterozygote
Homozygote
Humans
India
Interferon Regulatory Factors / genetics*
Introns / genetics
Male
Open Reading Frames / genetics*
Point Mutation / genetics
Sequence Analysis, DNA
Serine / genetics
Syndrome
Thymine
Chemical
Reg. No./Substance:
0/3' Untranslated Regions; 0/IRF6 protein, human; 0/Interferon Regulatory Factors; 56-45-1/Serine; 65-71-4/Thymine; 71-30-7/Cytosine; 73-24-5/Adenine; 73-40-5/Guanine; 74-79-3/Arginine

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  The need for orthognathic surgery in patients with repaired complete unilateral and complete bilater...
Next Document:  Effects of neonatal handling on playfulness by means of reversal of the desire to play in rats (Ratt...