| Clivus chordoma in a 9-year-old child: case report and review of the literature. | |
MedLine Citation:
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PMID: 3152925 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Chordomas are bone tumors of the axial skeleton. They arise from notochordal remnants. In children these tumors are extremely rare and are predominantly located in the skull base. The authors report on a clivus chordoma in a 9 7/12-year-old girl. It presented as a nasopharyngeal mass with destruction of the clivus and paralyses of the ninth, tenth, and eleventh cranial nerves on the right side. After incomplete resection by a transoral transclival route, high-dose radiotherapy was added. This treatment was effective as demonstrated by follow-up CAT scans. A short review of the current literature is given. The local recurrence rate is extremely high, and distant metastases may occur. Complete resection is rarely possible, and combined management with postoperative radiotherapy is propagated. Permanent cure is rare, and at the present time, chemotherapy appears to be of no value in the primary treatment of chordomas. |
Authors:
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F M Fink; B Ausserer; W Schröcksnadel; A K Pallua; H Frommhold; G Mikuz |
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Publication Detail:
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Type: Case Reports; Journal Article; Review |
Journal Detail:
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Title: Pediatric hematology and oncology Volume: 4 ISSN: 0888-0018 ISO Abbreviation: Pediatr Hematol Oncol Publication Date: 1987 |
Date Detail:
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Created Date: 1990-11-15 Completed Date: 1990-11-15 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 8700164 Medline TA: Pediatr Hematol Oncol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 91-100 Citation Subset: IM |
Affiliation:
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Department of Pediatrics, University of Innsbruck, Austria. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Child Chordoma* / complications, radiography, radiotherapy, surgery Combined Modality Therapy Cranial Nerve Diseases / etiology Female Humans Nerve Compression Syndromes / etiology Occipital Bone Prognosis Skull Neoplasms* / complications, radiography, radiotherapy, surgery Sphenoid Bone Tomography, X-Ray Computed |
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