Document Detail


Clinicopathological analyses of 5 Japanese patients with CD56+ primary cutaneous lymphomas.
MedLine Citation:
PMID:  11197216     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We analyzed the clinicopathological features of 5 Japanese patients with CD56+ primary cutaneous lymphomas (3 men and 2 women aged 25 to 73 years). Except for 1 patient in whom bone marrow involvement was simultaneously observed, all patients presented with cutaneous lesions. Based on their Epstein-Barr virus (EBV) status, we categorized these patients into 2 groups, namely EBV-encoded small RNA-1 (EBER-1) (3 patients) and EBER-1- (2 patients). Generalized lymphadenopathy and bone marrow involvement were observed only in EBER-1 patients. Morphologically, angiocentric proliferation was more prominent in EBER-1+ patients and was accompanied by panniculitis-like changes. The lymphomas in EBER-1- patients featured monomorphic proliferation of lymphoblastic cells with no cytoplasmic granules. Phenotypically, CD3-, cytoplasmic CD3 epsilon+, and CD56+ were common findings in both types. The EBER-1- type showed an additional distinguishing feature, CD7+, CD4+, CD8-, HLA-DR+, and terminal deoxynucleotidyl transferase-positive (TdT+) phenotype. The lymphoma was primarily resistant in the EBER-1+ type, and the patients died within 6 months of admission. In contrast, the lymphoma in the EBER-1- patients was originally chemosensitive. Collectively, we consider there to be at least 2 types of CD56+ primary cutaneous lymphomas, corresponding to nasal-type natural killer (NK)/T-cell lymphomas (EBER-1+) and blastic NK-cell lymphomas (EBER-1-).
Authors:
H Kojima; H Y Mukai; A Shinagawa; C Yoshida; M Kamoshita; T Komeno; Y Hasegawa; Y Yamashita; N Mori; T Nagasawa
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Publication Detail:
Type:  Comparative Study; Journal Article    
Journal Detail:
Title:  International journal of hematology     Volume:  72     ISSN:  0925-5710     ISO Abbreviation:  Int. J. Hematol.     Publication Date:  2000 Dec 
Date Detail:
Created Date:  2001-01-25     Completed Date:  2001-04-05     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  9111627     Medline TA:  Int J Hematol     Country:  Ireland    
Other Details:
Languages:  eng     Pagination:  477-83     Citation Subset:  IM    
Affiliation:
Division of Hematology, Institute of Clinical Medicine, University of Tsukuba, Tsukuba, Ibaraki, 305-8575, Japan. hkojima@md.tsukuba.ac.jp
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MeSH Terms
Descriptor/Qualifier:
Adult
Aged
Antigens, CD56*
Bone Marrow Neoplasms / etiology,  pathology
Female
Humans
Japan
Killer Cells, Natural / pathology
Lymphoma / classification,  pathology*,  virology*
Male
Middle Aged
Nose Neoplasms / etiology,  pathology,  virology
RNA, Viral / blood
Skin Neoplasms / immunology,  pathology,  virology*
T-Lymphocytes / pathology
Chemical
Reg. No./Substance:
0/Antigens, CD56; 0/Epstein-Barr virus encoded RNA 1; 0/RNA, Viral

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