Document Detail


Clinical syndromes of hormone receptor mutations: hormone resistance and independence.
MedLine Citation:
PMID:  8068885     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Clinical syndromes of hormone resistance or independence have baffled clinicians for decades. These syndromes sometimes result from mutations or deficiencies in enzymes that activate prohormones or from alterations in signal transduction proteins. The majority of these conditions, however, arise from abnormalities of hormone receptors. We describe examples of syndromes that result from genetic mutations or misexpression of steroid/thyroid hormone receptors, with a specific emphasis on thyroid and androgen resistance syndromes, and estrogen independence in breast cancer.
Authors:
R J Auchus; S A Fuqua
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Publication Detail:
Type:  Journal Article; Research Support, U.S. Gov't, P.H.S.; Review    
Journal Detail:
Title:  Seminars in cell biology     Volume:  5     ISSN:  1043-4682     ISO Abbreviation:  Semin. Cell Biol.     Publication Date:  1994 Apr 
Date Detail:
Created Date:  1994-09-29     Completed Date:  1994-09-29     Revised Date:  2007-11-14    
Medline Journal Info:
Nlm Unique ID:  9007587     Medline TA:  Semin Cell Biol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  127-36     Citation Subset:  IM    
Affiliation:
Department of Endocrinology, Wilford Hall Medical Center, Lackland AFB, TX 78236.
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MeSH Terms
Descriptor/Qualifier:
Animals
Endocrine System Diseases / etiology,  genetics*
Hormones / physiology
Humans
Mutation*
Receptors, Steroid / genetics*
Receptors, Thyroid Hormone / genetics*
Syndrome
Grant Support
ID/Acronym/Agency:
CA 30195/CA/NCI NIH HHS; CA 52351/CA/NCI NIH HHS; P30 CA 54174/CA/NCI NIH HHS
Chemical
Reg. No./Substance:
0/Hormones; 0/Receptors, Steroid; 0/Receptors, Thyroid Hormone

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