Document Detail


Clinical and radiological findings in Schinzel-Giedion syndrome.
MedLine Citation:
PMID:  18461363     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The absence of a definitive genetic test for the autosomal recessive condition Schinzel-Giedion syndrome is a significant handicap to the recognition of this disorder. Radiological features have been an important aspect of many of the published cases. In a series of six cases, we now establish a consistency among many of the radiological features in affected cases which will be an important diagnostic aid in identifying future cases. This is confirmed by reference to an extensive review of previously published instances of the syndrome. Moreover, the clinical data, including previously unpublished photographs, which we detail from our patients will assist in enhanced diagnosis in the future.
Authors:
Mudaffer Al-Mudaffer; Christine Oley; Sue Price; Ian Hayes; Alison Stewart; Christine M Hall; William Reardon
Related Documents :
1994883 - Toothpick injuries to the gastrointestinal tract.
19821203 - Temporal variation in manometric findings in achalasia: a case report.
12761643 - Pilocytic astrocytomas with leptomeningeal dissemination: biological behavior, clinical...
Publication Detail:
Type:  Case Reports; Journal Article     Date:  2008-05-07
Journal Detail:
Title:  European journal of pediatrics     Volume:  167     ISSN:  1432-1076     ISO Abbreviation:  Eur. J. Pediatr.     Publication Date:  2008 Dec 
Date Detail:
Created Date:  2008-10-20     Completed Date:  2009-02-05     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  7603873     Medline TA:  Eur J Pediatr     Country:  Germany    
Other Details:
Languages:  eng     Pagination:  1399-407     Citation Subset:  IM    
Affiliation:
Our Lady's Hospital for Sick Children, Crumlin, Dublin 12, Ireland.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / diagnosis,  radiography*
Craniofacial Abnormalities / complications,  diagnosis,  radiography*
Female
Fingers / abnormalities,  radiography
Humans
Hypertrichosis / etiology
Infant
Infant, Newborn
Limb Deformities, Congenital / etiology,  radiography
Male
Nails, Malformed / etiology
Pelvic Bones / abnormalities,  radiography
Syndrome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Complicated parapneumonic effusion in Belgian children: increased occurrence before routine pneumoco...
Next Document:  Levels of VEGF-A mRNA in plasma from patients with colorectal carcinoma as possible surrogate marker...