Document Detail


Clinical Utility of Functional Imaging with 18F-FDOPA in Von Hippel-Lindau Syndrome.
MedLine Citation:
PMID:  22259055     Owner:  NLM     Status:  Publisher    
Abstract/OtherAbstract:
Context:Von Hippel-Lindau (VHL) syndrome is an inherited cancer syndrome in which patients are at risk of developing multiple tumors in different organs. 6-L-(18)F-fluorodihydroxyphenylalanine ((18)F-FDOPA) positron emission tomography (PET) is a relatively new metabolic imaging tracer proposed for the use of localizing sites of neuroendocrine tumors. There are limited data on the clinical utility of using (18)F-FDOPA PET for identifying neuroendocrine tumors in a high-risk population such as VHL.Objective:The aim of this prospective study was to evaluate the clinical utility of (18)F-FDOPA PET in patients with VHL-related tumors.Design:Radiological findings were prospectively collected from four imaging modalities: computed tomography, magnetic resonance imaging (MRI), (18)F-fluorodeoxyglucose PET, and (18)F-FDOPA PET. (18)F-FDOPA PET findings were compared with those from other imaging modalities, as well as with clinical and laboratory data, and pathology findings if patients underwent an operation.Results:In 52 patients with VHL, 390 lesions were identified by computed tomography (n = 139), MRI (n = 117), (18)F-fluorodeoxyglucose PET (n = 94), and (18)F-FDOPA PET (n = 40). (18)F-FDOPA PET identified 20 pancreatic and 20 extrapancreatic tumors, including lesions in the adrenal gland (n = 11), kidney (n = 3), liver (n = 4), lung (n = 1), and cervical paraganglioma (n = 1). These tumor sites were not seen by conventional imaging studies in 9.6% of patients and 4.4% of lesions. Seven of eight patients who had an (18)F-FDOPA PET-positive lesion underwent resection, and pathology showed a neuroendocrine tumor. Four of 10 patients with positive adrenal uptake had elevated catecholamine levels, and six of 10 patients had a discrete mass on axial imaging.Conclusions:(18)F-FDOPA PET is a useful complementary imaging study to detect neuroendocrine tumors in patients with VHL undergoing surveillance, especially in those suspected to have adrenal pheochromocytoma or unusual ectopic locations.
Authors:
Allison B Weisbrod; Mio Kitano; Krisana Gesuwan; Corina Millo; Peter Herscovitch; Naris Nilubol; W Marston Linehan; Electron Kebebew
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Publication Detail:
Type:  JOURNAL ARTICLE     Date:  2012-1-18
Journal Detail:
Title:  The Journal of clinical endocrinology and metabolism     Volume:  -     ISSN:  1945-7197     ISO Abbreviation:  -     Publication Date:  2012 Jan 
Date Detail:
Created Date:  2012-1-19     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0375362     Medline TA:  J Clin Endocrinol Metab     Country:  -    
Other Details:
Languages:  ENG     Pagination:  -     Citation Subset:  -    
Affiliation:
Endocrine Oncology Section, Surgery Branch (A.B.W., M.K., K.G., N.N., E.K.), National Cancer Institute, National Institutes of Health, Bethesda, Maryland 20892; Department of Nuclear Medicine (C.M., P.H.), Positron Emission Tomography Imaging Section, National Institute of Health, Bethesda, Maryland 20892; and Urologic Oncology Branch (W.M.L.), National Cancer Institute, National Institutes of Health, Bethesda, Maryland 20892.
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